405 3 Flashcards
Disease with decreased or missing clotting factor
Hemophilia
Hemophilia inheritance
Male child inherits gene from mother
Female child is a carrier of the disease
Hemophilia patients should be immunized against
Hep B
Hemophilia: 3 preventions of dental injuries
Use a soft tooth brush
Regular flossing
Prophyllactic factor administration
Hemophilia: avoid what OTC
aspirin
Hemophilia: avoid what activity
contact sports
Hemophilia: grooming
use electric razor
Hemophilia: blood drawing
apply firm pressure for 1 full minute, elevate extremity above heart
Hemophilia: what common medical procedure should you avoid
IM injection
RICE
Rest
Ice
Compression
Elevation
increases factor VIII activity in hemophilia A
Desmopressin
If a Hemophilia patient has a mild injury they may be prescribed
Desmopressin
If a Hemophilia patient has a serious injury they may be prescribed
Replacement factors via IV or PICC line
Patient’s receive both treatments Desmopressin and missing/low factor based on
blood tests (factor assay)
subluxation
head of femur slips out of socket
subluxation is found in what condition
Congenital Dysplasia of Hip
Congenital Dysplasia of Hip is related to
fetal position in utero
Congenital Dysplasia of Hip: birth presentation was probably
breech
Ortolani’s Sign
Hip click
Barlow’s Sign
palpation of acetabulum (hip socket) slipping back & forth
Congenital Dysplasia of Hip: findings of the affected side
extra folds and shorter leg
Triple Diapering
hip dysplasia tx
hip dysplasia tx: ___ harness
Pavlik Harness
hip dysplasia tx: period ___ exams
radiology
hip dysplasia tx: wear the support structures for
23 hours a day
Talipes Equinovarus
Club Feet
Club Feet: occurrence
congenital
Club Feet: tx can include Manual manipulation using
short leg casts during early infancy
Club Feet: it may need to be treated with some kind of cast or brace; be sure to ___ child to promote normal G/D
stimulate
Scoliosis causes can be ___ or ___
idiopathic or congenital
Scoliosis: in cases where there’s a congenital cause, the specific cause might be ___ __ or ___ ___
spina bifida
cerebral palsy
Scoliosis: brace is worn how much?
18 hours a day
Neural Tubes Defects basic definition:
Failure of spinal cord and meninges to close