tricuspid_atresia_flashcards

Question 1

What is the initial medical management for Tricuspid Atresia?

Answer 1

Maintain adequate flow through PDA with prostaglandin E1 infusion, cardiorespiratory support with O2 and mechanical ventilation, inotropes, and IV fluid.

Question 2

What is the first stage surgical management for Tricuspid Atresia in neonates?

Answer 2

Early palliation to maintain a secure supply of blood to the lungs at low pressure by Blalock-Taussig shunt insertion (between subclavian and pulmonary arteries) or pulmonary artery banding operation to reduce pulmonary blood flow if breathless.

Question 3

What is the second stage surgical management for Tricuspid Atresia at 3-6 months old?

Answer 3

Removal of shunt and direct anastomosis of SVC to right pulmonary artery (Glenn).

Question 4

What is the third stage surgical management for Tricuspid Atresia at 2-5 years old?

Answer 4

Direct venous pathway from IVC into pulmonary arteries (Fontan).

Question 5

What prophylaxis is needed after surgical management for Tricuspid Atresia?

Answer 5

Antibiotic prophylaxis.

Question 6

Why is complete corrective surgery not possible in most cases of Tricuspid Atresia?

Answer 6

Because there is only one functioning ventricle.