Hereditary_Spherocytosis_Flashcards
What is the management for neonates with Hereditary Spherocytosis?
Management for neonates with Hereditary Spherocytosis includes supportive care and potentially red blood cell transfusion, folic acid supplementation, and phototherapy or exchange transfusion if the baby has jaundice.
What supportive treatments are considered for neonates with Hereditary Spherocytosis?
Supportive treatments for neonates with Hereditary Spherocytosis include red blood cell transfusion, folic acid supplementation, and phototherapy or exchange transfusion if jaundice is present.
What treatments are considered for infants, children, and adults with Hereditary Spherocytosis?
Treatments for infants, children, and adults with Hereditary Spherocytosis include supportive care, red blood cell transfusion, folic acid supplementation (2-5 mg oral OD), and consideration of splenectomy with pre-operative vaccination for encapsulated bacteria, as well as cholecystectomy due to common gallstones.
What supplementation is recommended for patients with Hereditary Spherocytosis?
Folic acid supplementation (2-5 mg oral OD) is recommended for patients with Hereditary Spherocytosis.
What surgical interventions may be considered for patients with Hereditary Spherocytosis?
Surgical interventions for patients with Hereditary Spherocytosis may include splenectomy and cholecystectomy.
What prophylactic measure is recommended post-splenectomy in Hereditary Spherocytosis?
Post-splenectomy in Hereditary Spherocytosis, pneumococcal prophylaxis with oral penicillin is recommended.
What causes an aplastic crisis in Hereditary Spherocytosis and how is it managed?
An aplastic crisis in Hereditary Spherocytosis is caused by parvovirus B19 and is managed with blood transfusions.
