Duchenne_Muscular_Dystrophy_Flashcards COPY

1
Q

How does physiotherapy help in managing Duchenne Muscular Dystrophy?

A

Physiotherapy helps prevent contractures in patients with Duchenne Muscular Dystrophy.

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2
Q

What additional support is necessary for patients with Duchenne Muscular Dystrophy?

A

Exercise and psychological support are necessary for patients with Duchenne Muscular Dystrophy.

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3
Q

What surgeries may be required for Duchenne Muscular Dystrophy patients?

A

Tendoachilles lengthening and scoliosis surgery may be required for patients with Duchenne Muscular Dystrophy.

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4
Q

How do glucocorticoids help in Duchenne Muscular Dystrophy?

A

Glucocorticoids (e.g. prednisolone) may help delay wheelchair dependence in Duchenne Muscular Dystrophy.

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5
Q

What is the role of Ataluren in Duchenne Muscular Dystrophy?

A

Ataluren is a drug that restores dystrophin synthesis and has conditional licensing for patients 5 years and over.

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6
Q

Why might a dietician be indicated for patients with Duchenne Muscular Dystrophy?

A

A dietician may be indicated for gastric feeding, and Vitamin D and calcium supplementation may be necessary to prevent and treat bone fragility.

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7
Q

What symptoms indicate weakness of intercostal muscles in Duchenne Muscular Dystrophy?

A

Weakness of intercostal muscles may lead to nocturnal hypoxia, presenting with daytime headache, irritability, and loss of appetite.

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8
Q

What respiratory support might be needed for Duchenne Muscular Dystrophy?

A

Overnight CPAP may be indicated for respiratory support in Duchenne Muscular Dystrophy.

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9
Q

What treatments are considered if left ventricular ejection fraction drops in Duchenne Muscular Dystrophy?

A

If the left ventricular ejection fraction drops, cardioprotective drugs (e.g. carvedilol) and left ventricular assist devices may be considered.

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