flashcards_wilsons_disease
What scores are used to assess the severity of Wilson’s Disease?
Nazar score or Kings Wilson score.
What is the role of zinc in managing Wilson’s Disease?
Zinc blocks intestinal copper resorption.
What are the oral chelation therapies used for Wilson’s Disease?
Penicillamine or trientine.
What is the function of trientine in managing Wilson’s Disease?
Trientine increases urinary copper excretion.
Why is pyridoxine (vitamin B6) given to Wilson’s Disease patients?
To prevent peripheral neuropathy.
What dietary restrictions are recommended for Wilson’s Disease patients?
Reduce liver and shellfish intake.
How long may neurological improvement take in Wilson’s Disease?
Up to 12 months.
When is liver transplantation considered for Wilson’s Disease patients?
In children with end-stage liver disease.
