child health Flashcards
Hemophilia
Hemophilia
is an inherited X-linked recessive disorder
(female carriers pass the defect to affected males).
Often diagnosed after client has abnormal,
prolonged bleeding following minor trauma
(circumcision, first fall)
Signs of bleeding: .
Notify the HCP if a client with hemophilia develops a decreased level of consciousness,
which can indicate cerebral bleeding, or black, tarry stools, which can indicate GI bleeding
Prevent bleeding:
To prevent bleeding,
clients with hemophilia should wear protective
equipment during physical activity and avoid
aspirin and contact sports.
Factor replacement:
To control active bleeding,
administer factor replacement to replace the
deficient clotting factor (VIII or IX).
Hemarthrosis:
If the client has joint swelling,
pain, and stiffness, the nurse should suspect
hemarthrosis and implement RICE: Rest, Ice,
Compression, and Elevation of the extremity.
Epistaxis management:
To stop bleeding from
epistaxis, the client should sit upright, lean
forward, apply pressure to the nostrils, and apply
ice or a cold compress to the nose and face.