child health

Question 1

CF is an inherited autosomal
recessive mutation of ion channels that alters chloride and water transport
in exocrine (mucus-producing) glands.

Answer 1

The child must inherit two copies of the gene (one from each parent) to have CF.

Question 2

Mobilizing secretions:

Answer 2

Administering
bronchodilators before performing airway
clearance therapies (CPT, PEP) helps mobilize
secretions.

Question 3

Malnutrition:

Answer 3

Provide a high-calorie, high-
protein diet and supplemental fat-soluble vitamins (A, D, E, K) to meet increased nutrient
requirements.

Question 4

Notify HCP for complications:

Answer 4

Decreased
activity and decreased appetite are subtle signs
of respiratory infection. Abdominal pain and
distension are signs of intestinal obstruction.

Question 5

Pancreatic enzyme replacement therapy (PERT):

Answer 5

Administer PERT within 30 minutes of eating to improve absorption of fats, proteins,
and carbohydrates.

Question 6

Psychosocial support:

Answer 6

Encourage participation
in physical activities like sports as tolerated and connect the client and family with
community resources like support groups.