Phospholipid and Glycolipid Metabolism Pt. II Flashcards
Ganglioside Function
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/606/a_image_thumb.png?1475698085)
Biosynthesis of GM1
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/641/a_image_thumb.png?1475698107)
Glycosphingolipid Degredation
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/651/a_image_thumb.png?1475698160)
Which one of the following is another example of a lysosomal storage disease
Von Gierke Disease
Cori Disease
MCAD
Refsum
Pompe Disease
Pompe Disease — Build up of glycogen and loss of glucosidase activity in the lysosome.
Pathway I to Lactosyl Ceramide
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/721/a_image_thumb.png?1475698199)
Second Pathway to Lactosyl Ceramide
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/742/a_image_thumb.png?1475698227)
Lactosyl Ceramide to Ceramide
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/773/a_image_thumb.png?1475698252)
Second Pathway to Ceramide
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/818/a_image_thumb.png?1475698281)
Third Pathway to Ceramide
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/838/a_image_thumb.png?1475698299)
Common Features of the Sphingolipidoses
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/846/a_image_thumb.png?1475698325)
Generalized Gangliosidoses
Disease Name
Enzyme Efficiency
Elevated Lipid
Symptoms
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/905/a_image_thumb.png?1475698386)
Tay Sach’s Disease
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/136/998/a_image_thumb.png?1475698425)
Sandhoff’s Disease
Disease Name
Enzyme Efficiency
Elevated Lipid
Symptoms
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/137/009/a_image_thumb.png?1475698446)
Fabry’s Disease
Disease Name
Enzyme Efficiency
Elevated Lipid
Symptoms
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/137/398/a_image_thumb.png?1475698510)
Ceramide Lactoside Lipidosis
Disease Name
Enzyme Efficiency
Elevated Lipid
Symptoms
![](https://s3.amazonaws.com/brainscape-prod/system/cm/198/137/783/a_image_thumb.png?1475698560)