Cystic Fibrosis Flashcards
What is the classic presentation of cystic fibrosis in neonates?
Meconium ileus
Distal intestinal obstruction syndrome
Failure to thrive
Neonatal jaundice
What are the respiratory features of cystic fibrosis?
Nasal polyps
Frequent lower tract infections
What is given for viscous mucus in cystic fibrosis?
Dornase alpha, a mucoactive agent that is a daily nebuliser
Hypertonic saline nebulisers can also be given
What is key antibiotic prophylaxis?
Flucloxacillin to prevent staphylococcus aureus infection
How is pseudomas aeruginosa infection eradicated?
Oral ciprofloxacin
With nebulised colomycin antibiotic
What is used as an immunomoduator for patients with declining lung function?
Oral azithromycin
What are the auscultation findings for cystic fibrosis?
Bilateral coarse crackles due to thick mucus
