Intestinal Lymphangiectasia Flashcards

1
Q

What is it?

A

Dilation of the lymphatics as a primary condition or secondary due to lymphatic obstruction (malignancy or constructive pericarditis)

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2
Q

How does it present?

A

Hypoproteinaemia with ankle oedema

Steatorrhoea

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3
Q

How is it diagnosed?

A

Jejunal biopsy- primary form, dilated lacteals
Capsule endoscopy: white tipped villi
Serum immunoglobulin: reduced, low circulating lymphocytes

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4
Q

How is it treated?

A

Low fat diets
Fat soluble vitamins supplements and mid chain triglyceride supplements
Octreotide: good effect on primary cases

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