22 - 147 - VASCULAR MALFORMATIONS

Question 1

The following are syndromic disorders of capillary malformation except ______ .

A. Phakomatosis pigmentovascularis

B. Sturge-Weber Syndrome

C. Diffuse capillary malformation with overgrowth

D. Microcephaly-capillary malformation

Answer 1

D

Question 2

Which of the following describes venous malformation?

A. Red

B Flat to raised

C. Ulceration

D. D2-40 positive

Answer 2

B

Question 3

What is the gold standard therapy for capillary malformation?

A. Propanolol

B. Laser therapy

C. Watchful waiting

D. Excision

Answer 3

B

Question 4

50% of venous malformations are found on the __________ .

A. Lower extremities

B. Lumbosacral area

C. Upper extremities

D. Cervicofacial area

Answer 4

D

Question 5

__________ is commonly characterized by one large “dominant” VM lesion associated with multiple small, dark blue, nipple-like lesions, the latter being typically located on the palm and soles .

A. SWS

B. KTS

C. BRBN

D. Mafucci syndrome

Answer 5

C

Question 6

What syndrome has a pathognominic sign of persistence of a persistent embryonic vein located on the lateral side of the thigh?

A. Klippel-Trenaunay

B. CLOVES

C. Generalized lymphatic anomaly

D Gorham-Stout

Answer 6

A

Question 7

Which of the following is pathognomonic of AVM?

A Presence of a mass on imaging

B. Tortous vessels on ultrasonography

C. Aggregation of high-velocity arterial and pulsatile venous flow with low resistance on color Doppler

D Flow voids on MRI

Answer 7

D