18-6 Flashcards

1
Q

Choledochal cyst

A

Congenital dilation of common bile duct

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2
Q

Congenital dilation of common bile duct

A

Choledochal cyst

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3
Q

When/who do Choledochal cysts usually present in?

A

Female children

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4
Q

Symptoms of Choledochal cysts?

A

Jaundice and abdominal pain

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5
Q

Symptoms of Choledochal cysts?

A

Jaundice and abdominal pain

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6
Q

Kids with Choledochal cysts are at an increased risk to develop what conditions?

A

Stone formation
Stenosis
Pancreatitis
Obstructive biliary issues

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7
Q

What 3 things fall under the Fibropolycystic Disease category?

A

Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis

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8
Q

What 3 things fall under the Fibropolycystic Disease category?

A

Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis

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9
Q

Von Meyenburg Complexes

A

Bile duct hamartomas

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10
Q

Bile duct hamartomas

A

Von Meyenburg complexes

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11
Q

Caroli Disease

A

Multifocal cystic dilation of large intrahepatic bile ducts

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12
Q

Multifocal cystic dilation of large intrahepatic bile ducts

A

Caroli Disease

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13
Q

Caroli Syndrome

A

Multifocal cystic dilation of large intrahepatic bile ducts + Congenital hepatic fibrosis

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14
Q

Multifocal cystic dilation of large intrahepatic bile ducts + congenital hepatic fibrosis

A

Caroli Syndrome

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15
Q

Congenital hepatic fibrosis

A

Bands of collagenous tissue that form septa and divide the liver into islands

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16
Q

Bands of collagenous tissue that form septa and divide the liver into islands

A

Congenital hepatic fibrosis

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17
Q

Congenital hepatic fibrosis includes _____ shaped bile ducts imbedded in the fibrosis

A

Abnormally shaped bile ducts

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18
Q

Those with Congenital hepatic fibrosis are at an increased risk for?

A

Portal HTN and bleeding varices

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19
Q

Fibropolycystic Disease

A

Congenital malformations of the biliary tree

  1. Von Meyenburg Complexes
  2. Caroli Disease/Syndrome
  3. Congenital Hepatic Fibrosis
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20
Q

What causes Fibropolycystic Disease?

A

Ductal plate malformations due to the persistence of fetal periportal ductal plates

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21
Q

What is associated with Fibropolycystic Disease?

A

Renal polycystic disease

– Increased risk for cholangiocarcinoma

22
Q

2 causes of Impaired blood flow into the liver?

A
  1. Hepatic A. compromise

2. Portal vein obstruction

23
Q

Signs of Hepatic A. compromise?

A

Pale or hemorrhagic infarct of the liver

24
Q

Common causes of Hepatic A. compromise?

A

Neoplasia, polyarteritis nodosa, sepsis

25
Q

Symptoms of Portal vein obstruction?

A

Abdominal pain, portal HTN with ruptured esophageal varices

26
Q

Symptoms of Portal vein obstruction?

A

Abdominal pain, portal HTN with ruptured esophageal varices

27
Q

What can cause extrahepatic portal vein obstruction?

A

Idiopathic
Umbilical vein catheterization
Hypercoagulable states

28
Q

What usually causes small branch portal vein obstruction?

A

Schistosomiasis - parasites laying eggs that cause obstruction

29
Q

Schistosomiasis (parasites laying eggs) can cause?

A

Small branch portal vein obstruction

30
Q

Signs of small branch portal vein obstruction?

A

NONcirrhotic portal HTN

31
Q

NONcirhortic portal HTN

A

Small branch portal vein obstruction

32
Q

Most common cause of impaired blood flow through the liver?

A

CIRRHOSIS

33
Q

Most common cause of impaired blood flow through the liver?

A

CIRRHOSIS

34
Q

Besides cirrhosis, what is another condition where blood flow is impaired through the liver?

A

Peliosis Hepatitis

35
Q

Peliosis Hepatitis

A

Sinusoidal dilation where EFFLUX of hepatic blood is impeded

36
Q

Peliosis Hepatitis

A

Sinusoidal dilation where EFFLUX of hepatic blood is impeded

37
Q

What will the liver contain with Peliosis Hepatitis?

A

Blood-filled cystic spaces

– sinusoidal dilation where EFFLUX of hepatic blood is impeded

38
Q

What conditions may cause Peliosis hepatitis?

A

AIDs - bartonella species
Cancer
TB
Sex hormone administration

39
Q

2 causes of Hepatic venous outflow obstruction?

A

Hepatic vein thrombosis

Sinusoidal obstruction syndrome

40
Q

Hepatic vein thrombosis =

A

Budd-Chiari syndrome

41
Q

Symptoms of Hepatic Vein Thrombosis (budd-chiari syndrome)?

A

Abdominal pain, ascites, hepatomegaly

42
Q

Symptoms of Hepatic Vein Thrombosis (budd-chiari syndrome)?

A

Abdominal pain, ascites, hepatomegaly

43
Q

In what 2 settings can Sinusoidal obstruction syndrome occur?

A
  1. Following allogenic HSC transplant

2. Cancer pts on chemotherapy

44
Q

Symptoms of Sinusoidal obstruction syndrome?

A

Ascites, hepatomegaly, weight gain and jaundice

45
Q

Symptoms of Sinusoidal obstruction syndrome?

A

Ascites, hepatomegaly, weight gain and jaundice

46
Q

What will a doppler US see with Sinusoidal obstruction syndrome?

A

Reversed/attenuated hepatic venous flow

47
Q

Preeclampsia

A

Maternal HTN, proteinuria, peripheral edema and coagulation abnormalties

48
Q

Preeclampsia

A

Maternal HTN, proteinuria, peripheral edema and coagulation abnormalities

49
Q

Signs of Preeclampsia?

A

HELLP

  • Hemolysis
  • Elevated Liver enzymes
  • Low Platelets
50
Q

Signs of Preeclampsia?

A

HELLP

  • Hemolysis
  • Elevated Liver enzymes
  • LOW platelets
51
Q

Eclampsia

A

Maternal HTN, proteinuria, peripheral edema, coagulation abnormalities +
Hyperreflexia and convulsions

52
Q

Eclampsia

A

Maternal HTN, proteinuria, peripheral edema, coagulation abnormalities +
Hyperreflexia and convulsions