18-6 Flashcards
Choledochal cyst
Congenital dilation of common bile duct
Congenital dilation of common bile duct
Choledochal cyst
When/who do Choledochal cysts usually present in?
Female children
Symptoms of Choledochal cysts?
Jaundice and abdominal pain
Symptoms of Choledochal cysts?
Jaundice and abdominal pain
Kids with Choledochal cysts are at an increased risk to develop what conditions?
Stone formation
Stenosis
Pancreatitis
Obstructive biliary issues
What 3 things fall under the Fibropolycystic Disease category?
Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis
What 3 things fall under the Fibropolycystic Disease category?
Von Meyenburg Complexes
Caroli Disease/Syndrome
Congenital Hepatic Fibrosis
Von Meyenburg Complexes
Bile duct hamartomas
Bile duct hamartomas
Von Meyenburg complexes
Caroli Disease
Multifocal cystic dilation of large intrahepatic bile ducts
Multifocal cystic dilation of large intrahepatic bile ducts
Caroli Disease
Caroli Syndrome
Multifocal cystic dilation of large intrahepatic bile ducts + Congenital hepatic fibrosis
Multifocal cystic dilation of large intrahepatic bile ducts + congenital hepatic fibrosis
Caroli Syndrome
Congenital hepatic fibrosis
Bands of collagenous tissue that form septa and divide the liver into islands
Bands of collagenous tissue that form septa and divide the liver into islands
Congenital hepatic fibrosis
Congenital hepatic fibrosis includes _____ shaped bile ducts imbedded in the fibrosis
Abnormally shaped bile ducts
Those with Congenital hepatic fibrosis are at an increased risk for?
Portal HTN and bleeding varices
Fibropolycystic Disease
Congenital malformations of the biliary tree
- Von Meyenburg Complexes
- Caroli Disease/Syndrome
- Congenital Hepatic Fibrosis
What causes Fibropolycystic Disease?
Ductal plate malformations due to the persistence of fetal periportal ductal plates