Right to Left Shunts

Question 1

Describe persistent truncus arteriosus? What defect is accompanied?

Answer 1

Truncus arteriosus fails to divide into the pulmonary trunk and aorta. BSD.

Question 2

In what defect is there a complete separation of systemic and Pulmonary circulations?

Answer 2

Transposition of great vessels.

Question 3

What defect has a boot-shaped heart on CXR?

Answer 3

Tetralogy of fallot

Question 4

In what defect is there a hypoplastic RV that requires both an ASD and a VSD for viability?

Answer 4

Tricuspid atresia AKA tricuspid valve absence

Question 5

What defect is caused by lithium exposure in utero?

Answer 5

Ebstein anomaly

Question 6

In what defect is there an egg on a string appearance on CXR?

Answer 6

Transposition of great vessels

Question 7

What defect is caused by anterosuperior displacement of the infundibular septum?

Answer 7

Tetralogy of fallot

Question 8

In what defect must a shunt be introduced at birth for viability?

Answer 8

Transposition of great vessels

Question 9

What defect is the most common cause of Early Childhood cyanosis?

Answer 9

Tetralogy of fallot

Question 10

In what defect do pulmonary veins drain into the right heart circulation and is associated with an ASD or sometimes a PDA?

Answer 10

Total anomalous pulmonary venous return (TAPVR)

Question 11

what defect is associated with tet spells, systolic murmur, and RA hypertrophy?

Answer 11

Tetralogy of fallot

Question 12

What defect is associated with a 22q 11 syndrome?

Answer 12

Tetralogy of fallot

Question 13

In what defect is a tricuspid valve leaflets downwardly displaced into the RV, artificially “aterializing” the ventricle?

Answer 13

Ebstein anomaly

Question 14

What defect is associated with tricuspid regurgitation, accessory conduction Pathways, right sided heart failure?

Answer 14

Ebstein anomaly

Question 15

What four defects are found in tetralogy of fallot?

Answer 15

Pulmonary infundibular stenosis, right ventricular hypertrophy, overriding aorta, VSD

Question 16

VSD, PDA, ASD, tetralogy of fallot is associated with what?

Answer 16

Fetal alcohol syndrome

Question 17

PDA, pulmonary artery stenosis, septal defects are associated with what?

Answer 17

Congenital rubella

Question 18

AV septal defect, VSD, ASD are associated with what?

Answer 18

Down syndrome

Question 19

Transposition of great vessels and VSD are associated with what?

Answer 19

Infant diabetic mother

Question 20

Aortic regurgitation, MVP, thoracic aortic aneurysm/dissection are associated with what?

Answer 20

Marfan syndrome

Question 21

Ebstein anomaly is associated with what?

Answer 21

Lithium exposure in utero

Question 22

Bicuspid aortic valve, coarctation of aorta are associated with what?

Answer 22

Turner syndrome

Question 23

Supravalvular aortic stenosis is associated with what?

Answer 23

Williams syndrome

Question 24

Truncus arteriosus, tetralogy of fallot are associated with what?

Answer 24

22 q11 syndromes

Question 25

Displacement of tricuspid valve leaflets downward into RV, artificially “atrializing” the ventricle. Associated with tricuspid regurgitation, accessory conduction pathways, and right-sidedHF.

Answer 25

Ebstein’s Anomaly