Right to Left Shunts Flashcards
Describe persistent truncus arteriosus? What defect is accompanied?
Truncus arteriosus fails to divide into the pulmonary trunk and aorta. BSD.
In what defect is there a complete separation of systemic and Pulmonary circulations?
Transposition of great vessels.
What defect has a boot-shaped heart on CXR?
Tetralogy of fallot
In what defect is there a hypoplastic RV that requires both an ASD and a VSD for viability?
Tricuspid atresia AKA tricuspid valve absence
What defect is caused by lithium exposure in utero?
Ebstein anomaly
In what defect is there an egg on a string appearance on CXR?
Transposition of great vessels
What defect is caused by anterosuperior displacement of the infundibular septum?
Tetralogy of fallot
In what defect must a shunt be introduced at birth for viability?
Transposition of great vessels
What defect is the most common cause of Early Childhood cyanosis?
Tetralogy of fallot
In what defect do pulmonary veins drain into the right heart circulation and is associated with an ASD or sometimes a PDA?
Total anomalous pulmonary venous return (TAPVR)
what defect is associated with tet spells, systolic murmur, and RA hypertrophy?
Tetralogy of fallot
What defect is associated with a 22q 11 syndrome?
Tetralogy of fallot
In what defect is a tricuspid valve leaflets downwardly displaced into the RV, artificially “aterializing” the ventricle?
Ebstein anomaly
What defect is associated with tricuspid regurgitation, accessory conduction Pathways, right sided heart failure?
Ebstein anomaly
What four defects are found in tetralogy of fallot?
Pulmonary infundibular stenosis, right ventricular hypertrophy, overriding aorta, VSD
VSD, PDA, ASD, tetralogy of fallot is associated with what?
Fetal alcohol syndrome
PDA, pulmonary artery stenosis, septal defects are associated with what?
Congenital rubella
AV septal defect, VSD, ASD are associated with what?
Down syndrome
Transposition of great vessels and VSD are associated with what?
Infant diabetic mother
Aortic regurgitation, MVP, thoracic aortic aneurysm/dissection are associated with what?
Marfan syndrome
Ebstein anomaly is associated with what?
Lithium exposure in utero
Bicuspid aortic valve, coarctation of aorta are associated with what?
Turner syndrome
Supravalvular aortic stenosis is associated with what?
Williams syndrome
Truncus arteriosus, tetralogy of fallot are associated with what?
22 q11 syndromes
Displacement of tricuspid valve leaflets downward into RV, artificially “atrializing” the ventricle. Associated with tricuspid regurgitation, accessory conduction pathways, and right-sidedHF.
Ebstein’s Anomaly
