Hypoplastic Left Heart Syndrome

Question 1

Hypoplastic L heart syndrome

Answer 1

L side of the heart is underdeveloped, diminishing the ability for systemic circulation

Question 2

Perfusion changes

Answer 2

blood from lungs going to the L atrium is obstructed, so blood flows through the ASD to the right side of the heart –> R ventricle pumps blood to the lungs and systemic circulation through the PDA

Question 3

VS changes

Answer 3

Increased HR/RR, hypothermia

Question 4

Treatment to keep ductus arteriosus open

Answer 4

administer prostaglandin

Question 5

Primary treatment

Answer 5

heart transplant

Question 6

Palliative 3 stage treatment

Answer 6

Norwood procedure, bidirectional glenn procedure, modified fontan procedure

Question 7

Norwood procedure

Answer 7

reconstruction of aorta through small tube allowing blood flow to the lungs

Question 8

When is the Norwood procedure done

Answer 8

right away

Question 9

Bidirectional glenn procedure

Answer 9

increases blood flow to the lungs by connecting the superior vena cava to the R pulmonary artery

Question 10

When is the bidirectional glenn procedure done

Answer 10

6 months

Question 11

Modified fontan procedure

Answer 11

conduit placement, connect inferior vena cava to pulmonary artery for blood flow to the lungs