Cardiology 8.3: Congenital heart defects Flashcards

1
Q

What is the most common congenital heart defect?What causes it?

A

VSDfetal alcohol syndrome

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2
Q

VSD: A left to right or right to left shunt? Why?

A

left to right bc the pressure in the systemic circuit is greater than going back to the RV, so it does

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3
Q

large VSD –> increase in blood flow to pulm circuit –> _____ –> Eisenmenger syndrome –> cyanosis

A

pulm HTN

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4
Q

Why do pts with Eisenmenger Syndrome get RVH?

A

increased pressure in pulmonary vascular circuit

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5
Q

Why do pts with Eisenmenger Syndrome get polycythemia?

A

deoxygenated blood in the systemic circuit causes hypoxemia –> epo released

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6
Q

Why do pts with Eisenmenger Syndrome get clubbing?

A

systemic cyanosis

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7
Q

What is the most common type of ASD?

A

ostium secundum

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8
Q

Which ASD is associated with Down Syndrome?

A

ostium primum

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9
Q

What direction is the blood shunted in ASD?

A

L to R

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10
Q

What heart sounds are heard with ASD?

A

split S2

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11
Q

What is a complication of ASD?

A

paradoxical emboli

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12
Q

PDA is associated with ____.

A

congenital rubella

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13
Q

____ is associated with congenital rubella.

A

PDA

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14
Q

The ductus arteriosus connects the ____ to the _____.

A

pulmonary artery to the aorta

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15
Q

The _____ connects the pulmonary artery to the aorta in fetal life.

A

ductus arteriosus

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16
Q

Which way does blood flow in the fetal ductus arteriosus?

A

from L to R (aorta to pulm artery)

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17
Q

When will a PDA present? How?

A

later in life with lower extremity edema

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18
Q

What is the murmur for PDA?

A

machine-like holosystolic murmur

19
Q

Why is the cyanosis in PDA in the lower extremities and not the upper?

A

bc the ductus arteriosus connects to the aorta after the aortic arch and its branches

20
Q

What is the tx for PDA? How does it work?

A

indomethacindecreases PGE

21
Q

What keeeeeps the PDA open?

A

prostaglandin E (PGE)

22
Q

Which direction is the blood shunted in Tetrology of Fallot?

23
Q

How and when does Tetrology of Fallot present?

A

cyanosis at birth (early)

24
Q

Dx?Juv pt squats after running around

A

Tetrology of Fallot

25
Why does squatting help Tetrology of Fallot pts feel better?
it increases arterial vascular resistance, preventing blood from entering the aorta (decreased shunting) and pushes it instead into the lungs (increased afterload)
26
Dx?boot-shaped heart on CXR
Tetrology of Fallot
27
What is the tx for transposition of the great vessels?
create a shuntex: keep PDA open with PGE
28
What causes transposition of the great vessels?
maternal diabetes
29
How does transposition of the great vessels present?
early cyanosis
30
What problem in embryology causes truncus arteriosus?
the truncus fails to divide
31
How do pts with truncus arteriosus present?
early cyanosis
32
What is the problem in truncus arteriosus?
there is not separation of the pulm artery and aorta- there's just one huge vessel coming off the ventricles
33
What causes tricuspid atresia?
failure of the tricuspid valve orifice to develop (and therefore the R ventricle, too)
34
What other problem is associated with tricuspid atresia?
ASD
35
How do tricuspid atresia pts present?
early cyanosis
36
What is coarctation of the aorta?
narrowing of the aorta
37
The infantile form of coarctation of the aorta is associated with \_\_\_\_\_.
a PDA (Turner's Syndrome)
38
Where is an infantile coarctation of the aorta found?
distal to the aortic arch but proximal to the PDA
39
How does infantile coarctaton of the aorta present?
as lower extremity cyanosis
40
What heart findings are present in Turner syndrome?
infantile coarctation of the aortabicuspid aortic valvePDA
41
How does adult form coarctation of the aorta present?
HTN in upper extremities and hypotension in lower extremities
42
What is the adult form of coarctation of the aorta associated with?
bicuspid aortic valve
43
What is the CXR finding for the adult form of coarctation of the aorta?
notched ribs