Respiratory 7 - Interstitial Lung Disease

Question 1

define interstitial lung disease

Answer 1

fibrosis of lung parenchyma - scarred + stiff

Question 2

diagnosing interstitial lung disease

Answer 2

high res CT

ground glass

biopsy if cause unclear

Question 3

6 aspects of treating interstitial lung disease

Answer 3

treat cause
stop smoking
phsyio 
pneumococcal+flu vax
advanced care planning
home oxygen

Question 4

summarise idiopathic pulmonary fibrosis

Answer 4

usually 50+
can’t identify cause

bibasal fine crackles, finger clubbing

5 year life expectancy

new drugs to slow progression include pirfenidone + nintedanib

Question 5

4 drugs that can cause pulmonary fibrosis

Answer 5

amiodarone
cyclophosphamide
methotrexate
nitrofurantoin

Question 6

4 secondary causes of pulmonary fibrosis

Answer 6

A1AT def
rheumatoid arthritis
SLE
systemic sclerosis

Question 7

what is hypersensitivity pneumonitis and how is it dealt with?

Answer 7

also called extrinstic allergic alveolitis

all the ‘x lung’ conditions

do BAL to confirm

remove allergen, give oxygen + steroid

Question 8

cryptogenic organising pneumonia

Answer 8

rare

focal inflammation of piece of lung

looks like pneumonia
confirmed by biopsy
need IV steriods

Question 9

asbestosis 4 features

Answer 9

lung fibrosis
pleural thickening + plaques
adenocarcinoma
mesothelioma