Paeds: Pulmonary Stenosis: congenital heart disease Dr Clarke

Question 1

Pathology

Answer 1

Acyanotic

Out flow obstruction Valves leaflets partially fused giving RV restricted outflow. (More common in Noonans syndrome)

Question 2

Symptoms

Answer 2

-small number of neonates have duct dependent pulmonary circulation

Question 3

Signs

Answer 3

-ESM L sternal edge
\+/- thrill
-soft or absent P2
-severe lesion- prolonged R V impulse with delayed pulmonary valve closure on auscultation.
*no carotid thrill
- R ventricular heave

Question 4

CXR shows

Answer 4

normal or post stenotic dilatation of pulmonary artery.

Question 5

ECG

Answer 5

RVH

Question 6

Rx

Answer 6

Transcatheter balloon dilatation