Pediatrics Flashcards
Pediatrics
Microcornea
clear cornea of normal thickness with a diameter less than 9 mm in the newborn and less than 10 mm after 2 years of age
AD,AR
همراهی های میکروکورنه آ
cataracts colobomas high hyperopia cornea plana PFV oculodentodigital syndrome Warburg micro syndrome Ehlers Danlos syndrome
Keratoglobus
AR
bilateral
noninflammatory
G
It may be seen in
Keratoglobus
Keratoglobus is a very rare autosomal recessive, bilateral noninflammatory condition present at birth.
It may occur in Ehlers-Danlos syndrome type VIB. The corneal curvature is steep, with thinning of the
cornea in the periphery and a very deep anterior chamber. Spontaneous breaks in
همراهی های کراتوگلوبوس؟
Ehlers-Danlos syndrome type VIB
steep cornea
thinning of the cornea in the periphery
very deep AC
Spontaneous breaks in Descemet(➡️acute cornea edema)
the cornea is easily ruptured by minor blunt trauma
Keratoconus
central or paracentral cornea bulges and progressively thins
progress during the adolescent years
همراهی های KCN
Down syndrome
atopic diseases
chronic eye rubbing
iron lines, stress lines (Vogt striae), and apical scarring
are often seen in which one?
Keratoconus or keratoglobus
Keratoconus
میکروفتالمی،کلوبوم،دیسپلازی رتین همراه با جزایر فراوانی از غضروف های داخل چشمی
تریزومی۱۳
در مورد blanc syndrome-dechaume bounnet کدام صحیح است؟
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