Pathoma: Renal Neoplasia

Question 1

The incidence of angiomyolipomas is increased among those with ______________.

Answer 1

tuberous sclerosis

Question 2

What are angiomyolipomas?

Answer 2

Hamartomas of the kidney

Question 3

What tissue does clear cell carcinoma arise from?

Answer 3

The epithelium of the tubules

Question 4

Other than small cell carcinoma, what other type of cancer can have paraneoplastic syndrome?

Answer 4

Renal cell clear cell carcinoma

Question 5

VHL is a ____________.

Answer 5

tumor suppressor

Question 6

Those with von Hippel-Lindau syndrome get __________ in addition to renal cell clear cell carcinoma.

Answer 6

hemangioblastomas of the cerebellum

Question 7

What are the three tissues that Wilms tumors recapitulate?

Answer 7

Blastemas
Tubules and glomeruli
Stroma

Question 8

What are the symptoms of WAGR?

Answer 8

Wilms tumors
Aniridia
Genital abnormalities
Retardation

Question 9

What are the symptoms of Beckwith-Wiedemann syndrome?

Answer 9

Hemitrophic muscular hypertrophy
Organomegaly of the oropharynx (especially tongue)
Wilms tumors
Neonatal hypoglycemia