Systemic JIA Flashcards

1
Q

what is systemic JIA?

A

an idiopathic inflammatory condition that causes arthritis and systemic symptoms.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

what are the symptoms?

A
Subtle salmon pink erythematous rash 
high swinging fever 
enlarged lymph nodes 
weight loss 
joint inflammation and pain
splenomegaly
muscle pain 
pleuritis
pericarditis
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What do blood results show?

A

Anti nuclear antibodies - negative.

Raised CRP, ESR, platelets and serum ferritin.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

what is a complication?

A

Macrophage activation syndrome - activation of the immune system.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

What are the signs of macrophage activation syndrome?

A
Disseminate intravascular coagulopathy
anaemia
thrombocytopenia
bleeding 
non blanching rash 
Low ESR 
Pancytopenic
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What are the differentials for children with a fever?

A

Systemic JIA
Kawasaki disease
rheumatic fever
leukaemia

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What is systemic JIA also known as?

A

Stills disease.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly