Systemic JIA Flashcards
1
Q
what is systemic JIA?
A
an idiopathic inflammatory condition that causes arthritis and systemic symptoms.
2
Q
what are the symptoms?
A
Subtle salmon pink erythematous rash high swinging fever enlarged lymph nodes weight loss joint inflammation and pain splenomegaly muscle pain pleuritis pericarditis
3
Q
What do blood results show?
A
Anti nuclear antibodies - negative.
Raised CRP, ESR, platelets and serum ferritin.
4
Q
what is a complication?
A
Macrophage activation syndrome - activation of the immune system.
5
Q
What are the signs of macrophage activation syndrome?
A
Disseminate intravascular coagulopathy anaemia thrombocytopenia bleeding non blanching rash Low ESR Pancytopenic
6
Q
What are the differentials for children with a fever?
A
Systemic JIA
Kawasaki disease
rheumatic fever
leukaemia
7
Q
What is systemic JIA also known as?
A
Stills disease.