ATI 19 - Cystic Fibrosis + Injury of Resp System + Pneumothorax Flashcards
1
Q
Cystic Fibrosis
A
inherited mutated gene
- characterized by thick, sludge-like secretion in all parts of body
- leads to mechanical obstruction of organs
2
Q
median lifespan
A
up to 40 yo
3
Q
risk factors
A
both biological parents w recessive trait
-caucasian
4
Q
cystic fibrosis
first signs
A
meconium ileus
child taste salty
5
Q
cystic fibrosis
upper resp symptoms
A
nasal congestion
sinusitis
6
Q
cystic fibrosis
lower resp symptoms
A
- chronic productive cough
- wheezing/crackles
- recurrent infections
- SOB
- exercise intolerance
- clubbing, barrel chest
7
Q
cystic fibrosis
pancreas symptoms
A
- vitamins ADEK deficiencies
- FTT or poor wt gain
- gluc intolerance d/t decr insulin productn
- enzyme supplements
8
Q
cystic fibrosis
GI symptoms
A
- constipatn + intestinal obstruction
- steatorrhea
- liver cirrhosis
- high cal diet
9
Q
cystic fibrosis
reproductive symptoms
A
- infertility
- low sperm count
- difficulty conceiving
10
Q
cystic fibrosis
sweat glands symptoms
A
- sweat chloride test is gold standard test
- salty sweat
- hyponatremia
11
Q
GI MGMT
A
- high protein, high cal diet
- 3 meal/day w snacks
- encourage oral fluids
- admin pancreatic enzymes w food
- ADEK vitamins
- laxative/stool softener
12
Q
how to determine adequate dosing for pancreatic enzymes
A
monitor stools
1-2 stools/day
13
Q
Injury to Respiration
patho
A
heat + smoke incr risk for airway obstruction fr edema
-can progress w/in hours
14
Q
Injury to Respiration
s/s
A
- burns around face + neck
- singe nose hair
- soot around mouth or nose
- hoarseness w stridor or voice change
- edema leading to airway obstruction, tachypnea, stridor, cough/wheeze
15
Q
carbon monoxide posioning
s/s
A
- headache/dizzy
- confusion
- SOB
- LOC
