Pediatric Pathology 3

Question 1

What’s the types of hyperbilirubinemia?

Answer 1

Question 2

Discuss predominantly unconjugated hyoerbilirubinemia

Answer 2

Question 3

Discuss predominantly conjugated hyperbilirubinemia

Answer 3

Question 4

Discuss the physiological neonatal jaundice

Answer 4

Question 5

Discuss pathological neonatal jaundice

Answer 5

Question 6

Discuss the hemolytic disease of newborn

Answer 6

Question 7

Describe the pathological features of hemolytic disease in a newborn

Answer 7

Question 8

Discuss the diagnosis of hemolytic disease of newborn

Answer 8

Question 9

Discuss treatment & prevention of hemolytic disease of a newborn

Answer 9

Question 10

Discuss type 1 Crigler Najjar Syndrome

Answer 10

Question 11

Discuss type 2 Crigler Najjar Syndrome

Answer 11

Question 12

Describe biliary atresia

Answer 12

Question 13

Discuss embryonal/fetal type biliary atresia

Answer 13

Question 14

Discuss perinatal type biliary atresia

Answer 14

Etiology: Nornally developed biliary tree is destroyed following birth by a virus induced injury to biliary epithelium

Onset of cholestasis: late (4-8 weeks)

Jaundice free period after physiological jaundice: present

Associated congenital anomalies: absent

Question 15

Discuss the morphology of biliary atresia

Answer 15

Question 16

Discuss the prognosis of biliary atresia

Answer 16

Question 17

Discuss idiopathic neonatal hepatitis

Answer 17

Question 18

Discuss the epidemiology, clinical features and prognosis of idiopathic neonatal hepatitis

Answer 18

Question 19

Discuss the morphology of idiopathic neonatal hepatitis

Answer 19

Question 20

What is Dubin-Johnson Syndrome?

Answer 20

Question 21

Describe the etiopathogenesis of Dublin-Johnson syndrome

Answer 21

Question 22

Discuss the clinical features Dubin-Johnson syndrome

Answer 22

Question 23

Discuss the morphology of Dublin Johnson syndrome

Answer 23

Question 24

What is rotor syndrome?

Answer 24

Question 25

What are the clinical features & pathological findings of rotor syndrome?

Answer 25

Question 26

What is Cystic fibrosis?

Answer 26

Question 27

Discuss etiopathogenesis of Cystic fibrosis

Answer 27

Question 28

What happens in the absence of CFTR?

Answer 28

Question 29

What happens to the lungs in cystic fibrosis?

Answer 29

Question 30

What does cystic fibrosis do to the pancreas?

Answer 30

Question 31

How does cystic fibrosis affect the liver?

Answer 31

Question 32

How does cystic fibrosis affected the reproductive tract?

Answer 32

Question 33

How does cystic fibrosis affect the meconium ileus ?

Answer 33

Question 34

Discuss the clinical features of cystic fibrosi

Answer 34

Question 35

How do we diagnose cystic fibrosis?

Answer 35

Question 36

What are the inborn errors of metabolism?

Answer 36