Immunology: Primary Immune Deficiencies Flashcards
Primary Immune Deficiencies:
What are the CD4, CD8, B Cell, IgM and IgG changes in:
- SCID
- Di George
- BLS
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Primary Immune Deficiencies:
What are the CD4, CD8, B Cell, IgM, IgG and IgA changes in:
- SCID
- Brutons
- Hyper IgM
- Selective IgA Deficiency
- CVID
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/092/a_image_thumb.png?1526934571)
Primary Immune Deficiencies:
What are the Neutrophil count, Leukocyte adhesion markers, Nitroblue test of oxidative killing (NBT) and pus findings in:
- Kostmann syndrome
- Leukocyte adhesion deficiency
- Chronic Granulomatous disease
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Primary Immune Deficiencies:
What is are the subclasses of Primary immune deficiencies?
“BACKLIT CHAMP R”
- B Lymphocyte Maturation
- Alternative pathway
- Classical pathway
- Killing
- Lymphoid progenitors
- Immune barriers
- Terminal common pathway/T Cell maturation/T Cell acitvation
- C3
- HAem stem cells
- Mannose binding lectin/Mobilisation of Phagocytes
- Phagocytosis
- Recruitment of other cells
Primary Immune Deficiencies:
What are the features, disease and disease characteristics of External epithelia deficiencies?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/095/a_image_thumb.png?1526934887)
Primary Immune Deficiencies:
What are the features, disease and disease characteristics of Mucosal surfaces deficiencies?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/097/a_image_thumb.png?1526938599)
Primary Immune Deficiencies:
What are the features, disease and disease characteristics of Commensal bacteria deficiencies?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/098/a_image_thumb.png?1526938622)
Primary Immune Deficiencies:
What are the features and disease characteristics of Reticular dysgenesis?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/099/a_image_thumb.png?1526938641)
Primary Immune Deficiencies:
What are the features and disease characteristics of Kostmann syndrome?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/100/a_image_thumb.png?1526936480)
Primary Immune Deficiencies:
What are the features and disease characteristics of Cyclic neutropenia?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/101/a_image_thumb.png?1526938695)
Primary Immune Deficiencies:
What are the features and disease characteristics of Leukocyte adhesion deficiency?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/102/a_image_thumb.png?1526938759)
Primary Immune Deficiencies:
What are the features, disease and disease characteristics of Phagocytosis deficiencies?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/103/a_image_thumb.png?1526938785)
Primary Immune Deficiencies:
What are the features and disease characteristics of Chronic granulomatous disease? Including:
- Absent respiratory burst
- Excessive inflammation
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/105/a_image_thumb.png?1526938832)
Primary Immune Deficiencies:
What are the features and disease characteristics of Chronic granulomatous disease? Including:
- Symptoms
- Investigations performed
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/107/a_image_thumb.png?1526938873)
Primary Immune Deficiencies:
What are the features, disease and disease characteristics of Recruitment of other cell deficiencies?
![](https://s3.amazonaws.com/brainscape-prod/system/cm/366/909/108/a_image_thumb.png?1526938905)