Lesson 4D (Part 2)

Question 1

Medullary sponge kidney

Answer 1

Dilated ectatic collecting tubules

Question 2

Is medullary spong kidney congenital?

Answer 2

Yes

Question 3

Is medullary sponge kidney symptomatic or asymptomatic?

Answer 3

Asymptomatic

- until the 30-40s

Question 4

What do renal stones cause? (4)

Answer 4

1. Renal colic
2. Hematuria
3. Dysuria
4. Flank pain

Question 5

What kind of disease is multicystic dysplastic?

Answer 5

Nonhereditary developmental anomaly

Question 6

What does multicystic dysplastic look like? (3)

Answer 6

1. Kidney is small
2. Malformed with multiple cysts
3. Little or no normal renal parenchyma

Question 7

Is multicystic dysplastic symptomatic or asymtomatic?

Answer 7

Asymptomatic

Question 8

Is multicystic dysplastic unilateral or bilateral?

Answer 8

Unilateral

- if bilateral it is incompatible with life

Question 9

What is 90% of cases of multicystic dysplastic associated with?

Answer 9

UT obstruction during embryogenesis

Question 10

MCKD1

Answer 10

Medullary cystic kidney disease

Question 11

Medullary cystic kidney disease

Answer 11

Is an inherited condition that leads to scarring of the kidney and cyst formation

Question 12

When do symptoms begin for MCKD1?

Answer 12

Adulthood

Question 13

What are the symptoms for MCKD1? (3)

Answer 13

1. Increased urine production
2. Polyuria
3. Nocturia

Question 14

What does MCKD1 result in?

Answer 14

Kidney failure

Question 15

What kind of tumour is multilocular cystic nephroma? (2)

Answer 15

1. Uncommon

2. Benign neoplasm

Question 16

What gender is multilocular cystic nephroma more common in?

Answer 16

Females

Question 17

What are the symptoms of multilocular cystic nephroma?

Answer 17

1. UTI abdominal pain
2. Hematuria
3. Hypertension
4. Asymptomatic
   - sometimes

Question 18

What does multilocular cystic nephroma look like on US? (3)

Answer 18

1. Multiseptated
2. Exophytic complex cystic mass
3. Noncommunicating locules

Question 19

What is not recommended for multilocular cystic nephroma?

Answer 19

Biopsy

Question 20

What is multilocular cystic nephroma confirmed with?

Answer 20

CECT

Question 21

What kind of disease is localized cystic disease? (3)

Answer 21

1. Rare
2. Benign
3. Nonhereditary

Question 22

What does multilocular cystic nephroma mimic?

Answer 22

Autosomal Dominant Polycystic Kidney Disease

Question 23

What is the parenchyma like between the conglomerate mass of cysts of varying size?

Answer 23

Normal or atrophic renal parenchyma

Question 24

What does not help in the diagnosis of localized cystic disease? (2)

Answer 24

1. Family history of ADPKD

2. Lack of cysts in other kidney

Question 25

What helps to diagnose localized cystic disease? (2)

Answer 25

1. CT

2. MRI

Question 26

What kind of disease is Von Hipple-Lindau disease?

Answer 26

Inherited disease

Question 27

What does 40% of people with Von Hipple-Lindau disease develop?

Answer 27

RCC

Question 28

Is Von Hipple-Lindau disease unilateral or bilateral?

Answer 28

Bilateral

Question 29

Is Von Hipple-Lindau disease multifocal?

Answer 29

Yes

Question 30

What are a common finding with Von Hipple-Lindau disease?

Answer 30

Renal cysts

Question 31

What is useful in the diagnosis of Von Hipple-Lindau disease?

Answer 31

1. US
2. CT and MRI
   - better for detection of small multifocal and bilateral tumors