peds104 Flashcards
decreased IgG, IgA, IgM, and IgE, along with absent or markedly decreased B cells
Brutton’s agammaglobulinemia
onset of recurrent bacterial infections in the first 5 yr of life; serum IgG, IgM, and IgA low; absent isohemagglutinins or poor response to vaccines; less than 2percent cd19 pos B cells
brutton’s agammaglobulinemia
boy with eczema, thrombocytopenia, and recurrent infections with encapsulated germs
wiskott-aldrich syndrome
presents at birth with petechiae, bruises, bleeding from circumcision, or bloody stools
wiskott-aldrich
low IgM, high IgA and IgE; poor antibody response to polysaccharide antigens, modertely reduced T cells and platelets
wisott-aldrich syndrome
recurrent and uncontrolled infections with catalase-pos organisms
chronic granulomatous disease
lymphadenitis, and abscesses of the skin and viscera (liver); lymphocytes are normal
chronic granulomatous disease
an immediate anaphylactic reaction, an encephalopathy, or any CNS complication within 7 days of DTAP, means do what for the next dose?
only give DT; the acellular pertussis is prob responsible so we hold off on that
by age 1 yo, what should weight and height be?
weight should triple and height should increase by 50 percent
twice daily administration of prophylactic penicillin should be given to kids with sickle ceel disease until hwen
5 years of age
infant with cyanosis that is aggravated by feeding nad relieved with crying
choanal atresia
management of choanal atresia
place an oral airway and lavage feeding; definitive treatment is repairing the obstruction with surgery or endoscopy
inspiratory stridor that is exacerbated by any exertion; symptoms appear in the first 2 weeks of life an dincrease in severity
laryngomalacia
caf au lait spts, macrocephaly, feeding problems, short stature, learning disabilities
NF type 1
bilateral acoustaic neuromas and cataracts
NF type 2
fine reticular granulatiry of the lung parenchyma
classic in hyaline membrane disease
chest xray shouws prominent pulmonary vascular markings,, fluid lines in the fissures, overaeration, a flat diaphragm, and occasionally pleural fluid
transient tachypnea of the newborn
persistent pulm htn of the newborn
cyanosis; persistence of fetal circulatory pattern of R to L shunting; hypoxia unresponsive to 100percent oxygen;
meconium aspiration can lead to pneumothorax or pneumodiastinum
right
patchy infiltrates, coarse streaking of both lung fields, increased anterposteriod diameter, and flattening of the diaphrag,
chest xray in meconium aspiration
osgood schlatters disease
aka traction apophysitis
what bacteria is associated with infants with indwelling IV catheters
coag neg staph
most common causes of early onset and late sepsis
GBS and E coli
hypotonia, hepatosplenomegaly, cervical lymphadenopath, protruding abdomen, cherry red spon on macula, regression of milestones
niemann-pick disease
