HIRSCHSPRUNG DISEASE Flashcards
other name of Hirschsprung Disease?
AGANGLIONIC MEGACOLON
what is Hirschsprung disease?
is an absence of ganglionic innervation to the muscle of a section of the bowel
what part in most instances does Hirschsprung disease happen?
the lower portion of the sigmoid colon just above the anus
stools passing through such a small, narrow segment
ribbonlike stools
occurs more often in what sex
males
symptoms of Hirschsprung disease become apparent when
6 to 12 months of age
diagnosis is further confirmed by a
rectal exam
a gloved finger inserted inti the rectum of a child with true constipation, what will the hand touch
hard and caked stool
is generally ordered to substantiate the diagnosis of Hirschsprung disease
barium enema or ultrasound with contrast mediums
a definitive diagnosis is obtained by
anorectal manometry
a technique that tests the strength or innervation of the internal rectal sphincter by inserting a balloon catheter into the rectum.
Anorectal manometry
repair of aganglionic megacolon involves
dissection and removal of the affected section, with anastomosis of the intestine (termed as a pull-through operation)
Treatment for Hirschsprung Disease
First, a temporary colostomy is established, followed by bowel repair at 12 to 18 months of age.