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PBR 2 and 3 > Page 11 > Flashcards

Page 11 Flashcards

1
Q

syndrome of multiple hamartomas including HAMARTOMATOUS polyposis of the GIT, with goiter and thyroid adenomas and increased risk of breast ca and TCC of the urinary tract, and with mucocutaneous lesions with facial papules, oral papillomas, and palmoplantar keratoses

A

Cowden disease

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2
Q

phakomatosis associated with colonic polyps, cutaneous tumors, meningioma, glioma, as well as thyroid and breast neoplasms; half of patients with dysplastic cerebellar gangliocytoma has this syndrome

A

Cowden sidease

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3
Q

inherited ADENOMATOUS polposis coli / FAP syndrome which includes a few polyps in the small bowel, with associated bone and skin abnormalities
including cortical thickening of the ribs and long bones, multiple osteomas of the skull, supernumerary teeth, exostoses of the mandible, and dermal fibromas; desmoids; and epidermal inclusion cysts

A

Gardner syndrome

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3
Q

aka hepatorenal fossa

A

Morison’s pouch

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3
Q

familial ADENOMATOUS polyposis syndrome with associated tumors of the CNS

A

Turcot syndrome

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3
Q

pathologic ring-like stricture at the level of the B ring, caused by reflux esophagitis

A

Schatzki ring

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3
Q

normal variant, elongated inferior tip of right lobe of liver, >women

A

Riedel lobe

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3
Q

association of cervical esophageal webs, IDA, and pharyngeal or esophageal ca

A

Plummer-Vinson syndrome or Paterson-Kelly syndrome

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3
Q

consists of 1) dlated small bowel loops, 2) air in biliary tree or gallbladder, and 3) calcified gallstones in ectopic location

A

Rigler triad

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3
Q

occur in the lower abdominal wall lateral to the rectus abdominis and inferior to the umbilicus through a defect in the aponeurosis of the transversus abdominis and internal oblique muscles

A

Spigelian hernias

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3
Q

systemic disorder affecting the GIT, joints, CNS, and LNs, which may present with arthritis, neurologic symptoms, or steatorrhea

A

Whipple disease

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3
Q

entrap only a portion of the bowel wall without compromising viability

A

Richter hernias

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3
Q

most common subtype (type IA) of glycogen storage disease to affect the liver

A

von Gierke’s disease

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3
Q

Bile duct hamartomas

A

von Meyenburg complexes

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3
Q

copper deposition

A

Wilson disease

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3
Q

acrocephalosyndactyly consisting of suture closure, midfacial hypoplasia, and symmetrical syndactyly of the hands and feet. Characteristic skull findings at birth are closed coronal suture and midline calvarial defect from glabella to the posterior fontanelle, producing a wide metopic suture area. Cerebral anomalies are common. Cervical spine fusion is common and almost always involves C5-C6 (vs C2-C3 in Crouzon’s syndrome)

A

Apert’s syndrome

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3
Q

caused by gastrin-secreting islet cell tumor (gastrinoma), resulting in unusually severe and refractory ulcer disease, accompanied by diarrhea

A

Zollinger-Ellison syndrome

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3
Q

craniofacial dysostosis; characterized by craniosynostosis, exophthalmos, and midface retrosuion. Other findings include prominent digital markings in the skull (>90%), stylohyoid ligament calcification, and nasal septal deviation. Maxilla is hypoplastic. Spinal anomalies usually consist of C2-C3 fusion.

A

Crouzon’s syndrome

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3
Q

acrocephalosyndactyly type 1 - craniosynostosis with hypertelorism, midface hypoplasia, and cervical spine anomalies; severe symmetric hand and foot syndactyly

A

Apert syndrome

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4
Q

mandibulofacial dysostosis; antimongoloid slant to the eyes, flat cheekbones, small mandible, dysplastic ears, deafness, coloboma, and deficient lashes in the lower eyelids. Radiographic findings: marked hypoplasia of the zygomatic arches, maxilla, and paranasal sinuses. Egg-shaped orbits. Sometimes, with external and middle ear involvement.

A

Treacher Collins syndrome

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4
Q

Enthesophyte that arises from the posteroinferior portion of the glenoid rim, often seen in baseball pitchers and probably arising at the site of insertion of the posterior band of the inferior glenohumeral ligament complex

A

Bennett’s lesion

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5
Q

fracture at the base of the thumb into the carpometacarpal joint

A

Bennett fracture

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6
Q

fracture of the base of the thumb that does not involve the joint

A

psuedo-Benett fracture

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6
Q

comminuted fracture of the base of the thumb that extends into the joint

A

Rolando fracture

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7
Q

normal anatomic landmark that if is narower than 20 deg is indicative of a compression/fracture of the calcaneus

A

Bohler angle

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7
Q

Fracture of the dorsal rim of the radius with intra-articular extension

A

Barton’s fracture

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7
Q

Fracture of the styloid process of the radius

A

Hutchinson’s / chauffeur’s fracture

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8
Q

Fracture of the distal radius with dorsal displacement

A

Colle’s / Pouteau’s fracture

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9
Q

variation of seatbelt injury demonstrating fracture through the spinous process

A

Chance fracture

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9
Q

Fracture of the distal radius with palmar / volar displacement; reverse Colle’s

A

Smith’s / Smith fracture

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9
Q

variation of seatbelt injury demonstrating fracture of the posterior body

A

Smith fracture

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9
Q

Combination of ulnar fracture and superior radial / radial head dislocation (GRIMUS)

A

Monteggia’s fracture-dislocation

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9
Q

Combination of radial fracture and inferior radioulnar dislocation (GRIMUS)

A

Galeazzi’s fracture-dislocation

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10
Q

condensed linear shadow on the lateral radiograph representing tangential bone in the intercondylar fossa

A

Blumensaat’s line

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10
Q

absent anterosuperior labrum in association with a thickened “cord-like” middle glenohumeral ligament

A

Buford complex

10
Q

neuropathic joint

A

Charcot joint

10
Q

severe arthropathy of CPPD mimicking a neuropathic or Charcot joint

A

pseudo-Charcot joint

10
Q

to the upper outer acetabular margin consists of rheumatoid arthritis, splenomegaly, and leukopenia

A

Felty’s syndrome

10
Q

indication of acetabular depth; angle formed by a perpendicular line through the midportion of the femoral head and a line from the femoral head center

A

center-edge angle of Wiberg

11
Q

bony irregularity or fragment off the inferior glenoid (same mechanism with Hill-Sachs)

A

Bankart deformity

11
Q

triad consisting of keratoconjunctivitis sicca, xerostomia, and connective tissue disease. Last feature may be identical to RA

A

Sjogren’s syndrome

11
Q

AI disorder characterized by sicca syndrome (dry eyes/keratoconjunctivitis sicca, dry mouth/xerostomia, and dry nose/xerorhinia) which results from

A

Sjogren syndrome

11
Q
A

Garre’s sclerosing osteomyelitis

11
Q

indentation on the posterosuperior portion of the humeral head; caused by the impaction of the humeral head on the inferior lip of the glenoid during a shoulder dislocation

A

Hill-Sachs deformity/lesion

11
Q

atlantoaxial subluxation in association with an inflammatory condition of the head and neck

A

Grisel’s syndrome

12
Q

burst fracture of C1

A

Jefferson’s fracture

13
Q

aka dancer’s fracture; avulsion of the base of the 5th metatarsal from a pull by the peroneus brevis tendon

A

Jones fracture

14
Q

erosive osteoarthritis; same distribution with primary osteoarthritis but with erosions and osteoporosis

A

Kellgren arthritis

15
Q

avascular necrosis of the carpal lunate

A

Kienbock malacia

16
Q

avascular necrosis of the tarsal navicular

A

Kohler disease

17
Q

avascular necrosis of the metatarsal heads

A

Freiberg infraction

18
Q

avascular necrosis of the ring of the epiphyses / apophyseal ring of the spine

A

Scheuermann disease

18
Q

avascular necrosis of the femoral head

A

Legg-Perthes disease

18
Q

fracture through large osteoid seams; pathognomonic for osteomalacia

A

Looser fracture / Looser’s zones

19
Q

avascular necrosis of the tibial tubercle (aka surfur knees)

A

Osgood-Schlatter disease

19
Q

delayed further collapse of a wedge compression fracture with severe neurologic deficits 1-2 weeks after trauma

A

Kummell disease

19
Q

meniscofemoral ligament that extends from the medial femoral condyle, passes in front of the PCL, and attaches to the posterior horn of the lateral

A

ligament of Humphrey

20
Q

meniscofemoral ligament that extends from the medial femoral condyle, passes behind the PCL, and attaches to the posterior horn of the lateral meniscus

A

ligament of Wrisberg

20
Q

fracture-dislocation of the tarsometatarsals

A

Lisfranc fracture

21
Q

triad: polyostotic fibrous dysplasia associated with cafe au lait spots on the skin and precocious puberty; assoc with pituitary adenomas

A

McCune Albright syndrome

22
Q

bilateral nodular adrenal hyperplasia

A

McCune-Albright syndrome

23
Q

mucopolysaccaridose characterized by abnormal storage and excretion in the urine of keratin sulfate

A

Morquio syndrome

24
Q

mucopolysaccaridose characterized by abnormal storage and excretion in the urine of heparan sulfate

A

Hurler syndrome

25
Q

multiple enchondromas or enchondromatosis

A

Ollier disease

26
Q

multiple enchondromas associated with soft tissue hemangiomas

A

Maffucci syndrome

27
Q

neurogenic edema is found in muscle groups that correspond to a particular nerve (ie, supra/infra=suprascapular nerve; teres minor/deltoid=axillary nerve)

A

Parsonage-Turner syndrome

28
Q

Triad of radiographic findings characteristic of TB arthritis

A

Phemister’s triad

28
Q

joint affliction occuring after minor trauma to an extremity, demonstrating severe patchy osteoporosis and ST swelling

A

Sudeck atrophy

29
Q

reactive arthritis

A

Reiter syndrome

29
Q
A

Salter epiphyseal fracture

30
Q

small, bony fragment pulled off the posterior lateral tibial joint line by an avulsion of the lateral joint capsule

A

Segond fracture

31
Q

(+) space between navicular/scaphoid and lunate

A

Terry Thomas sign

32
Q

another name for pyknodysostosis

A

Toulouse-Lautrec syndrome

32
Q

Voorhoeve disease

A

aka osteopathia striata which manifests multiple linear bands of sclerosis parallel to the long axis of the bone

33
Q

partial sacral agenesis, anorectal stenosis, and presacral mass

A

Currarino triad

34
Q

thymic aplasia, absence of the parathyroid glands, and cardiovascular anomalies; caused by faulty development of the 3rd and 4th pharyngeal pouches

A

DiGeorge syndrome

34
Q

one of the syndromes associated with short ribs and small thoracic cage

A

Ellis-van Creveld syndrome

35
Q

hepatoportoenterostomy

A

Kasai procedure

35
Q

vasculitis of unknown etiology that affects the skin, GIT, joint, and kidneys; abdominal pain and intestinal bleeding (50%)

A

Henoch-Schoenlein purpura

35
Q

hemangioendothelioma associated with thrombocytopenia due to sequestration of platelets within the tumor

A

Kasabach-Merritt syndrome

36
Q

mucocutaneous lymph node syndrome

A

Kawasaki disease

37
Q

peritoneal bands

A

Ladd bands

38
Q

utilized to determine the level at which the blind pouch ends on lateral radiographs. Line is drawn perpendicular to the long axis of the ischia on lateral view and passes through the junction between the middle and lower third of the ischia

A

M line of Cremin

39
Q

associated with bilateral renal agenesis, congenital renal cystic disease, or obstructive uropathy (posterior urethral valves, prune belly syndrome) resulting
in hypoplastic lungs

A

Potter syndrome

40
Q

triad of necrotizing granulomatous lesions in both the upper and lower respiratory tract, as well as glomerulonephritis

A

Wegener polyangitis

PBR 2 and 3 (41 decks)

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