Respiratory - Cystic Fibrosis Flashcards
What is cystic fibrosis?
An inherited condition caused by a mutation if a gene in chromosome 7 that controls movement of salts and water in and out of cells - causes a build up of mucus in lungs and digestive system
What are the symptoms of cystic fibrosis?
Reoccurring chest infections
Persistent inflammation of bronchioles
Coughing + wheezing
Shortness of breath
What is the cause of cystic fibrosis?
Defective gene on both chromosome 7 genes that make protein that controls movement of salts and water in + out of cells - CFTR gene - causes thick sticky mucus build up
How can cystic fibrosis be monitored?
Spirometry - nose clip, blow out - measures how fast and how much you can breathe out - check if meds are working
What are the benefits of spirometry?
Easy test - not too long
Support from GP
Results sent off = accurate
What are the cons of spirometry?
Make time to see GP
Wait for results
How can cystic fibrosis be treated?
Medications - steroids (reduce inflammation), antibiotics (treat secondary infection), mucolytic agents (thin mucus)
Physiotherapy - restore mobility and function
Exercise - breaks up mucus
Surgery - lung transplant
What are the benefits of physiotherapy/ exercise for CF?
Breaks down mucus - easier to cough up
Helps sleep and self esteem
Help mobility and strength
What are the cons of physiotherapy/ exercise for CF?
Long wait list on NHS
Need to do exercises regularly
Need to make time to go to appointments
Not a cure
What impacts does CF have on life?
No cure
Breathlessness = unable to leave house sometimes
Hospital stays
Time off school or work a lot
Life revolved around medications and treatments
Need to avoid illness’s
What are the care/support needs for CF?
School/ work understanding
PE breaks at school
Medications stored
Extra support at school
