Respiratory - Cystic Fibrosis Flashcards

1
Q

What is cystic fibrosis?

A

An inherited condition caused by a mutation if a gene in chromosome 7 that controls movement of salts and water in and out of cells - causes a build up of mucus in lungs and digestive system

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What are the symptoms of cystic fibrosis?

A

Reoccurring chest infections
Persistent inflammation of bronchioles
Coughing + wheezing
Shortness of breath

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What is the cause of cystic fibrosis?

A

Defective gene on both chromosome 7 genes that make protein that controls movement of salts and water in + out of cells - CFTR gene - causes thick sticky mucus build up

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

How can cystic fibrosis be monitored?

A

Spirometry - nose clip, blow out - measures how fast and how much you can breathe out - check if meds are working

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

What are the benefits of spirometry?

A

Easy test - not too long
Support from GP
Results sent off = accurate

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What are the cons of spirometry?

A

Make time to see GP

Wait for results

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

How can cystic fibrosis be treated?

A

Medications - steroids (reduce inflammation), antibiotics (treat secondary infection), mucolytic agents (thin mucus)
Physiotherapy - restore mobility and function
Exercise - breaks up mucus
Surgery - lung transplant

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

What are the benefits of physiotherapy/ exercise for CF?

A

Breaks down mucus - easier to cough up
Helps sleep and self esteem
Help mobility and strength

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

What are the cons of physiotherapy/ exercise for CF?

A

Long wait list on NHS
Need to do exercises regularly
Need to make time to go to appointments
Not a cure

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

What impacts does CF have on life?

A

No cure
Breathlessness = unable to leave house sometimes
Hospital stays
Time off school or work a lot
Life revolved around medications and treatments
Need to avoid illness’s

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

What are the care/support needs for CF?

A

School/ work understanding
PE breaks at school
Medications stored
Extra support at school

How well did you know this?
1
Not at all
2
3
4
5
Perfectly