PEDS resp exam 1 Flashcards
Multisystem disorder of exocrine glands
cystic fibrosis
Increased production of thick mucus in bronchioles, small intestines, and pancreatic and bile ducts
what is the etiology of cystic fibrosis?
Inherited autosomal recessive trait
Usually diagnosed in infancy and early childhood
Life expectancy increasing - >30 years now
what is the patho of cystic fibrosis?
Increased viscosity of secretions
Lungs – atelectasis
Clogged pancreatic ducts
Absence of pancreatic enzymes in small intestines – unable to absorb fats and protein
what is the diagnosis for cystic fibrosis?
Sweat test
72 hours fecal fat
Chest x-ray
Prenatal DNA of amniotic fluid
what is the nursing and s/s of cystic fibrosis?
History of frequent respiratory infections
S/SX: cough, sputum, dyspnea, decreased Sao2, crackles or wheezes in lungs, cyanosis, digital clubbing, bulky, frothy, foul-smelling stools (steatorrhea), meconium ileus
Assess: skin turgor, hydration status,
what is the nursing care for cystic fibrosis?
Provide high-calorie, high-protein foods
Administer pancreatic enzymes with all meals and snacks
Administer fat-soluble vitamins (A,E,D,K)
Avoid pulmonary treatments after meals to decrease the chance of vomiting
what are the meds for cystic fibrosis?
Antibiotics – treat pulmonary infection
Pancreatic enzymes – for fat absorption
Fat-soluble vitamins A,E,D,K
Mucolytics – to decrease viscosity of sputum
Bronchodilators – to improve lung function
what is the education for cystic fibrosis?
Avoid exposure to respiratory infections
Chest percussion and postural drainage
High-calorie and high protein diet
Activity and exercise will loosen secretions
Genetic counseling
what are your acquired resp probs?
Bronchopulmonary dysplasia (BPD)
Asthma
what is bronchopulmonary dysplasia (BPD)?
Chronic obstructive pulmonary disease occurring in infants after prolonged oxygen therapy and mechanical ventilation
Possible genetic predisposition
what is your patho for BPD?
High oxygen concentrations and mechanical ventilation damage bronchial epithelium and alveoli;
thickened alveolar walls, scarring, and fibrosis lead to atelectasis, poor airway clearance of mucus, and poor gas exchange;
chronic low oxygenation results in decreased lung compliance and altered function
What are the diagnosis and s/s of BPD?
Diagnosed by chest x-ray
ABGs reveal hypercapnia and respiratory acidosis
S/SX: tachypnea, tachycardia, increased work of breathing, retractions, wheezing, barrel chest, pallor, poor feeding, activity intolerance
what is the nursing care for BPD?
ICU
Intubation with mechanical ventilation
Suction, turn, and weigh carefully to ensure oxygen saturations are maintained
Monitor continuously; condition can deteriorate quickly
Monitor for fluid overload
Cluster nursing care
what are the meds for BPD?
Bronchodilators
Corticosteroids
Diuretics
Antibiotics
what is the fam education for BPD?
May be discharged with multiple needs
Teach parent CPR, use of home oxygen equipment, trach care, feeding
Review infection control practices
Referrals to community agencies
Chronic inflammatory disorder in which airways narrow and are hyperreactive to stimuli that do not affect nonasthmatic individuals.
asthma
what is the patho for asthma?
Exposure to irritants causes constriction of bronchial smooth muscle, edema, increased secretion of thick mucus, and airway narrowing;
Expirations through the narrowed lumen is impaired, resulting in air trapping and hyperinflation of the alveoli
Triggers
what is the diagnosis and s/s of asthma?
Chest x-ray and symptoms
Pulmonary Function Tests
Wheezing and dry cough, prolonged expiration, restlessness, fatigue, tachypnea, cyanosis, marked respiratory distress
Chronic use of accessory muscles for respiration leads to barrel chest
what is the nursing care for asthma?
Assess resp status, administer humidified oxygen prn, monitor pulse ox
Maintain IV access, avoid cold liquids to avoid bronchospasm
Position high-fowlers and cluster nursing care
Sudden cessation of wheezing and decreased breath sounds indicates worsening
what are the meds for asthma?
Bronchodilators
Anti-inflammatory agents (steroids)
IV fluids
Oxygen
what is the fam education for asthma?
Teach to identify and avoid potential triggers
Check peak flow daily
Keep rescue inhaler with patient at all times
what are infectious resp probs?
Acute laryngotracheobronchitis (LTB)
Epiglottitis
Pneumonia
Bronchiolitis