Hemophilia Flashcards
what is hemophilia ?
refers to a group of bleeding disorders resulting from a deficiency of specific coagulation proteins
In hemophilia, it is important to identify
the specific coagulation deficiency so that definitive treatment with the specific replacement agent can be implemented
aggressive replacement therapy is initiated to prevent the chronic crippling effects from joint bleeding
What are the most common types of hemophilia?
Factor VIII deficiency (Hemophilia A or classic hemophilia)
Factor IX deficiency (Hemophilia B or Christmas disease)
Primary treatment for hemophilia
replacement of the missing clotting factor
additional medications such as agents to relieve pain or corticosteroids may be prescribed depending on the source of bleeding from the disorder
Lab results that may be abnormal in hemophilia
results of tests that measure platelet function are normal; results of tests that measure clotting factor function may be abnormal
Should those with hemophilia play contact sports ?
No; risk of injury and bleeding
Hemophilia A is a deficiency of which clotting factor ?
Factor VIII
hemophilia A is also known as classic hemophilia