Fetal heart anomalies PT 2 Flashcards
What are 2 main anomalies to consider when the LV appears smaller than RV?
- Hypoplastic left heart syndrome
2. coarctation of the aorta
Hypoplastic left heart syndrome?
- Consists of a small LV with aortic atresia and MV hypoplasia or atresia
- The LA may be small or normal in size
- aortic valve is an imperforate membreane
- acsending aorta and arch are most often hypoplastic
Coarctation of the aorta?
- what is it?
- where does it occur?
- what is it due to?
- narrowing of the aortic lumen
- occurs between the insertion of the ductus arteriosus and lt subclavian artery
- due to a discrete shelf-like lesion in the aorta
what is most likely an ethology with RV smaller than LV?
PULMONARY ATRESIA
Pulmonary atresia?
- no flow from the RV through the pulmonary valve onto the main pulmonary artery
- main pulmonary artery may be normal in size or hypoplastic
Enlarged right atrium (Ebstein’s anomaly)?’
- what is it?
- what view is it visualized in?
- Inferior displacement of the septal and posterior leaflets of the tricuspid valve
- Tv usually incompetent leading to RT atria enlargement
- seen in 4CH view
ebstein’s anomaly may be associated with?
a variety of structural cardiocascular defect:
- Pulmonary atresia or stenosis
- arrhythmia
- chromosomal anomalies
Overriding aorta?
- the aorta displaced more to the right side and positioned over a VSD instead of left ventricle (causing mixing of oxygenated and deoxygenated blood)
- disrupts normal continuity of the ventricular septum and the wall of the aorta
what is a key structure to evaluate when an overriding aorta is seen?
pulmonary artery
Tetralogy of Fallot accounts for what % of CHD?
10%
What is the primary diagnosis to consider when overriding aorta is seen?
Tetralogy of Fallot
Tetralogy of Fallot consists of? (6)
- stenosis of the RVOT
2 Hyplastic or stenotic pulmonary artery - Abnormality of the pulmonary valve or annulus
- Infundibular stenosis (below the PA in the RV)
- Ventricular septal defect
- Overriding aorta
What is tetralogy of Fallot?
- hypertrophy of the right ventricle
- happens after birth
- RV works against resistance to flow due to pulmonary stenosis
What is the most important problem after birth associated with tetralogy of fallot?
systemic hypoxia
Truncus arteriosus?
- rare and a more severe form of TOF
- a single blood vessel (truncus arteriosus) comes out of the right and left ventricle, instead of two normal vessels (pulmonary artery and aorta)