Ear Reconstruction - Microtia - Trauma Flashcards
A 25-year-old woman has facial asymmetry. She says that she has had progressive loss of soft-tissue volume on the right side of the face since age 10 years that became stabilized four years ago. Examination shows significant subcutaneous atrophy of the right side of the face without bony asymmetry. She also has hypopigmentation of the iris on the affected side.
Which of the following is the most appropriate management?
(A) Bone graft augmentation of the midface
(B) Alloplastic augmentation
(C) Reconstruction with a microvascular serratus anterior free flap
(D) Reconstruction with a microvascular parascapular free flap
(E) Reconstruction with a superficial temporal fascia flap
The correct response is Option D.
This 25-year-old woman has Romberg’s hemifacial atrophy characterized by progressive unilateral loss of facial soft tissue. The underlying skeleton is also affected in patients with severe forms of the disease. Surgery should be delayed until the condition becomes stabilized, which is indicated by the cessation of facial atrophy. When this has occurred, a microvascular parascapular flap can be deepithelialized and customized to fit the dimensions of the defect, and then transferred and buried subcutaneously.
Skeletal augmentation with either bone graft or alloplast is not appropriate because the bones of the face are not affected. The serratus anterior flap would only atrophy over time, and the superficial temporal fascia flap would not provide the necessary volume.
Which of the following hormones is responsible for the success of molding therapy of ear deformities in the neonatal period?
(A) Estrogen
(B) Growth hormone
(C) Progesterone
(D) Prolactin
(E) Thyroid
The correct response is Option A.
At birth, the neonate’s ears are soft and pliable, which makes molding therapy of ear deformities more successful during the neonatal period. This pliability is thought to be due to the effect of maternal estrogen, which increases the amount of hyaluronic acid, a major constitute of ear cartilage. After six weeks, the infant’s estrogen level begins to fall, and the ears becomes firmer and less malleable. Because breast-fed infants have higher levels of estrogen for a longer time, their ears may be moldable for a longer period.
The other hormones have no effect on the pliability of cartilage in the newborn period.
Several studies reported success with different molding methods. One reported an 87% rate of success after treating 92 ears with soft putty and taping. The deformities treated included lop, prominent, Stahl’s, and constricted ears. Another study used flexible plastic tubing and wire to form splints and reported good results in 19 neonates. Children treated after three months of age showed little significant improvement. In both studies, complications were minimal.
A 35-year-old man has persistent enophthalmos 18 months after undergoing open reduction of a fracture of the orbital floor and zygoma. Forced duction testing shows no restriction of eye motion. Which of the following is the most likely cause of this patient’s enophthalmos?
(A) Fat atrophy
(B) Fibrosis of the extraocular muscles
(C) Herniated contents of the orbit within the maxillary sinus
(D) Inadequate fracture reduction
(E) Scar contracture
The correct response is Option D.
Persistent enophthalmos following facial trauma is primarily caused by increased bony orbital volume secondary to inadequate fracture reduction. An appropriate anatomic reduction should be the initial goal of surgery; bone grafting may be required to restore orbital volume to normal levels.
Fat atrophy, extraocular muscle fibrosis, herniation of orbital contents, and scar contracture can also contribute to the discrepancy between traumatic and nontraumatic orbital volume, but are less likely to contribute to postoperative enophthalmos than inadequate fracture reduction. In addition, extraocular muscle fibrosis and/or scarring would typically be associated with limited motion of the globe on forced duction testing.
A 2-week-old female infant is evaluated because of a prominent ear deformity. Which of the following is the most appropriate early management to address this deformity?
A) Cartilage grafting
B) External molding
C) Injection of hyaluronidase
D) Otoplasty
E) No intervention at this time
The correct response is Option B.
External molding is the early treatment of choice for a prominent ear deformity. Ideally, this is started by 2 weeks of age, but improvement has been seen in patients up to 3 months of age and is worth trying. Splinting is a shorter therapy used for Lop ear and Stahl ear deformation. Injectable chondroplasty using hyaluronidase is still in the trial phase, but if effective, would allow molding to be used in children older than 3 months of age. Otoplasty at 6 years of age is the alternative if molding therapy is unsuccessful.
A 21-year-old man sustains a complete amputation of the right ear at the level of the external auditory canal in a motor vehicle collision. There are no other injuries. Which of the following procedures will provide the best aesthetic result?
(A) Delayed total ear reconstruction with a rib cartilage graft
(B) Dermabrasion of the epidermis of the amputated ear, burial of the ear in a subcutaneous postauricular pocket, followed by removal and coverage with a skin graft or flap
(C) Removal of the skin of the amputated ear, reattachment of the ear cartilage, and immediate coverage with a temporoparietal fascial flap and skin graft
(D) Composite grafting of the amputated ear followed by surface cooling
(E) Microsurgical ear replantation
The correct response is Option E.
Successful microsurgical replantation of the ear provides superior aesthetic results while eliminating the need for other complex reconstructive procedures. However, this technique is associated with increased operative time and the need for multiple blood transfusions. Hospitalization is typically prolonged, and failure rates associated with the procedure are high.
Delayed reconstruction results in only moderate cosmetic improvement, and secondary reconstruction does not sufficiently recreate the intricate architecture of the external ear.
Primary nonvascularized replantation of the ear produces a good appearance initially because of the survival of the avulsed cartilage; however, late distortion of the cartilage frequently limits the overall aesthetic result. Techniques used for nonvascularized replantation include primary reattachment of the ear with surface cooling, dermabrasion of the ear, and partial or complete burial of the ear in a postauricular skin pocket, followed by coverage of the filleted cartilage with a temporoparietal fascial flap and skin graft.
A 6-year-old girl with prominent ears due to overdeveloped conchae and effaced antihelical folds is scheduled to undergo otoplasty by a combination of methods including Stenstrom cartilage abrasion. In this technique, which of the following surfaces of the auricular cartilage is abraded?
(A) Anterior surface of the antihelix
(B) Anterior surface of the conchal bowl
(C) Lateral border of the helix
(D) Posterior surface of the antihelix
(E) Posterior surface of the conchal bowl
The correct response is Option A.
Classic congenital prominence of the ears is caused by an overdeveloped or excessively deep conchal bowl; an underdeveloped, effaced, or absent antihelical fold; or both. Surgical correction of prominent ears commonly calls for a combination of procedures, including the Mustardé technique for placement of mattress sutures to create an antihelical fold, partial excision of the conchal bowl, placement of concha-mastoid sutures for setback of the conchal bowl, and Stenstrom cartilage abrasion.
Stenstrom cartilage abrasion requires partial thickness scoring, scratching, or abrading of the anterior surface of the antihelix. This causes the cartilage to bend away from the abraded surface, creating or accentuating an antihelical fold.
To correct prominent ears, projection of the conchal bowl usually needs to be reduced by excision or by setback with placement of concha-mastoid sutures, not by scoring the anterior or posterior surface. Because the helix is normal in prominent ears, it should not be abraded.
During second-stage ear reconstruction with elevation of the costal cartilage framework, a temporoparietal flap is elevated to cover a cartilage block. The blood supply of this flap most commonly comes from which of the following arteries?
A) Angular
B) Maxillary
C) Occipital
D) Posterior auricular
E) Superficial temporal
The correct response is Option E.
Elevation of the ear reconstruction framework can be covered by using a temporoparietal flap (TPF) if needed. The most common blood supply of the TPF is typically the superficial temporal artery but less frequently can be the posterior auricular artery or the occipital artery branches. The TPF flap can be safely raised on these less common pedicles as needed.
A 15-year-old boy undergoes reconstruction of a 15-mm2 traumatic defect of the right ear with a graft harvested from the contralateral ear. On examination two days after the procedure, the graft appears dusky. A photograph is shown above. Which of the following is the most appropriate next step in management?
(A) Hyperbaric oxygen therapy
(B) Application of leeches
(C) Release of the sutures
(D) Debridement of the graft

The correct response is Option A.
In this 15-year-old boy who exhibits duskiness at the graft site two days after undergoing composite grafting of the ear, the most appropriate next step is initiation of hyperbaric oxygen therapy. This will provide oxygenation during the critical ischemia period for the graft and thus is likely to improve the outcome. Hyperbaric oxygen therapy enhances antimicrobial activity by facilitating the oxidative burst of polymorphonuclear neutrophils. It increases the hyperoxygenation of tissue to a level that is 10 to 15 times greater than normal. In addition, it stimulates angiogenesis and blunts the ischemia-reperfusion injury response.
Application of leeches is appropriate if arterial input is adequate but venous outflow is insufficient, as in patients undergoing microsurgical replantation who demonstrate thrombosis of the vein, or if a suitable vein does not exist for anastomosis. However, duskiness of the ear is an indication of arterial insufficiency, and leeches would fail to attach if they were applied.
Because a composite graft receives its vascularity through diffusion from the surrounding wound bed, releasing the sutures would inhibit the “take” of the graft to the bed. Similarly, performing debridement two days after grafting is excessive. Instead, the composite graft should be left in place for a minimum of two weeks in order to demonstrate healing and incorporation, as long as infection does not develop.
A 70-year-old man who underwent total resection of the right ear followed by radiation because of squamous cell carcinoma one year ago comes to the office for consultation regarding reconstruction of the ear. He says he needs the ear to support his eyeglasses. Medical history shows chronic obstructive pulmonary disease. Which of the following reconstruction techniques is most appropriate in this patient?
(A) Fixation of autogenous cartilage under local flaps
(B) Implantation of osseointegrated auricular prostheses
(C) Placement of porous polyethylene framework and coverage with a radial forearm free flap
(D) Placement of silicone rubber (Silastic) framework and coverage with a temporoparietal flap
(E) Tissue expansion and placement of porous polyethylene framework
The correct response is Option B.
Ear reconstruction techniques are needed to address a variety of congenital, traumatic, and ablative defects. Both an intricate framework and stable covering are needed to obtain a consistent and aesthetically pleasing reconstruction. Cartilage has been the framework of choice for many years, but this involves some donor morbidity. Silastic and porous polyethylene frameworks offer synthetic alternatives but can become infected or exposed. Covering can be accomplished by local tissue if available, expanded tissue, and local or distant skin flaps.
Prosthetic ears have been available for many years but were limited by the harsh adhesives necessary to keep them in place. The use of osseointegrated titanium implants for the retention of dental prostheses opened a new possibility for implant fixation in other areas of the body.
Several recent studies document the recommended indications for autogenous versus prosthetic techniques. One study of 98 patients recommends autogenous reconstruction for pediatric microtia patients and prosthetic reconstruction for traumatic or ablative defects in adults. In addition, prosthetic ears are also recommended for severe soft tissue hypoplasia, low or unfavorable hairline, and failed autogenous reconstruction. Another study of 55 patients recommended autogenous reconstruction for classic microtia, relatively normal lower one third of the ear, patient preference, and noncompliant patients. The principal indications for osseointegrated implants were major cancer extirpation, poor local tissue, absence of the lower half of the ear, salvage following unsuccessful surgery, and poor operative risk patients.
In this case of an older patient with medical problems and poor local tissue, the fastest and safest option is a prosthetic ear implant. His radiation would preclude tissue expansion or a temporoparietal flap. A rib donor site would have significant morbidity in a patient with chronic obstructive pulmonary disease. A free flap is also high risk in this patient, with its longer anesthetic time and need for anticoagulation.
An otherwise healthy 3-day-old term female infant is brought to the clinic for evaluation of a prominent ear deformity. The parents are interested in nonsurgical options, and they would like to pursue ear molding but are concerned about the complications associated with molding devices. The parents should be advised that the most common complication of such devices is which of the following?
A) Chondritis
B) Otitis media
C) Overcorrection
D) Sensorineural hearing loss
E) Skin ulceration
The correct response is Option E.
Although all of the answers are potential complications of treatment with ear molding, the most common complication is skin ulceration. In a recent study, skin ulceration occurred at a rate of 7.6%. Other studies have reported the rate of skin ulceration around 3%. Although chondritis and allergy to adhesives are complications, their rates were lower than 3 to 7.6%. Since this is an external system, it should not impact eustachian tube dysfunction. Ear molding does not contribute to hearing loss. Overcorrection is not likely with molding alone.
The antihelix and antitragus of the external ear arise from which of the following embryologic structures?
A) First branchial arch
B) First branchial groove
C) First pharyngeal pouch
D) Second branchial arch
E) Second branchial groove
Development of the six branchial arches occurs within the walls of the anterior foregut during the fourth week of gestation, as neural crest cells migrate into the future head and neck region and alternating ridges and depressions develop. A series of clefts forms during embryologic development to create the branchial grooves externally and the pharyngeal pouches internally.
The auricle arises from the first (mandibular) and second (hyoid) branchial arches and is further defined by the development of six hillocks, which appear on these arches during the sixth week of gestation. The anterior (first through third) hillocks give rise to the tragus, root of the helix, and superior helix. The posterior (fourth through sixth) hillocks give rise to the posterior helix, antihelix, antitragus, and lobule. Meckel’s cartilage is derived from the first branchial arch; it ossifies to form the malleus and incus. The external acoustic meatus develops from the first branchial groove. The middle ear and eustachian tube are formed from the first pharyngeal pouch. Reichert’s cartilage is also derived from the second branchial arch and ossifies to form the stapes. The second, third, and fourth branchial grooves are obliterated within the cervical sinus during the later stages of development.
Which of the following congenital ear deformities is characterized by absence of the superior auriculocephalic sulcus?
(A) Cryptotia
(B) Cup ear deformity
(C) Lop ear
(D) Microtia
(E) Prominent ear deformity
The correct response is Option A.
Cryptotia (“hidden ear”) is a congenital deformity of the cartilage of the scapha and antihelix. In neonates who have this deformity, the upper pole of the ear is buried beneath the scalp, and the superior auriculocephalic sulcus is absent. Conservative management is most appropriate initially; surgical release should be performed when the child is older.
Infants with the cup ear deformity have hooding of the scapha and helix and flattening of the antihelix. Lop ear is characterized by protrusion of the ear and folding of the superior helix. Microtia is a hypoplastic condition that manifests as varying degrees of ear absence, from anotia (complete ear absence) to a smaller than normal ear with normal morphology. The prominent ear deformity involves widening of the conchoscaphal angle, increased auriculocephalic distance, and loss of the antihelical fold.
A 55 year old woman is referred to the office by her primary physician because she has had a painful, chronic area of scabbing on the right ear for the past three months. Physical examination shows a 2 x 1-mm area of skin ulceration on the superior helix of the ear. Surrounding inflammation and exposed cartilage are noted. Which of the following is the most appropriate initial step in management?
(A) Daily wound dressing with bacitracin ointment and avoidance of pressure on the ear
(B) Excision with 5-mm margins and coverage with a retroauricular trap door flap
(C) Excision with 5-mm margins and reconstruction with an Antia €‘Buch advancement flap
(D) Excisional biopsy and primary wound closure
(E) Injection of triamcinolone and daily topical application of hydrocortisone cream
The correct response is Option D.
The patient described most likely has a benign condition referred to as chondrodermatitis nodularis helicis, an inflammation of the cartilage of the ear that often leads to a painful open area. This condition can mimic a skin cancer on physical examination. Unless the area is clearly benign, biopsy is warranted to rule out skin cancer. Recurrence rate for this condition is high. Excisional biopsy and primary wound closure will give a pathological confirmation and may suffice as treatment.
Daily wound dressing with bacitracin ointment or injection of triamcinolone and daily topical application of hydrocortisone cream are both inappropriate because neither would give the appropriate tissue diagnosis. Excision and reconstruction or coverage with a flap are unwarranted given no pathological diagnosis.
Chondrodermatitis nodularis helicis is a condition of unknown etiology predominantly found in older men and often is associated with trauma from sleeping. It begins as an area of cartilage inflammation and then ulcerates through the skin. The treatment is excision of the cartilage and closure of the skin. Recurrence rates remain high. Preventive measures to decrease the recurrence rate include avoidance of sleeping on the affected ear.
A healthy 7-year-old boy with anotia undergoes reconstruction of the right ear via implantation of a high-density porous polyethylene prosthesis. Compared with use of autologous cartilage, which of the following is the most likely result of this procedure?
A) Higher incidence of contour deformities
B) Higher incidence of extrusion
C) Increased likelihood of malposition
D) Lower incidence of infection
E) More resorption of the implant over time
High density porous polyethylene (Medpor) is an alloplastic implant material that is nonresorbable and highly biocompatible. It has an intramaterial porosity with a pore size between 125 and 250 μm, which permits extensive fibrovascular ingrowth throughout the implant. Although limited bony ingrowth may occur in select clinical circumstances, the material should not be considered truly osteoconductive. This bony and fibrovascular ingrowth can make this type of material somewhat difficult to remove. Studies have shown less underlying bone resorption occurs with high density polyethylene than with other implant materials.
As an alloplastic material, it should not be placed in contaminated wound beds, because it can get easily infected, and should always be positioned in areas of adequate soft tissue cover to prevent extrusion. The incidence of extrusion is higher in microtia reconstruction and nasal dorsum augmentation for this reason.
A 16 €‘year €‘old boy who underwent costochondral reconstruction of the right ear 20 days ago because of microtia has had pain, erythema, fluctuance, and swelling of the ear as well as fever for the past 48 hours. A photograph is shown. In addition to intravenous administration of an antibiotic, which of the following is the most appropriate management?
(A) Application of mafenide acetate (Sulfamylon)
(B) Incision and drainage, washout, and placement of irrigating drains
(C) Incision and removal of the cartilage construct and placement of irrigating drains
(D) Needle aspiration and application of a compressive bolster dressing
(E) Observation

The correct response is Option B.
The clinical scenario described is dire because of the likely loss of the costochondral ear reconstruction. The cartilage may have gained enough vascularity to help avoid loss of the construct. In addition to intravenous administration of an antibiotic, incision and removal of the construct must be considered, but a trial of incision and drainage, washout, and placement of irrigating drains is warranted in an attempt to avoid loss of this graft. If the fever and cellulitis do not improve quickly, then removal of the construct is warranted as a secondary procedure.
Application of Sulfamylon, needle aspiration, and observation are not aggressive enough for this severe infection.
A 58-year-old woman is scheduled to undergo bilateral upper eyelid blepharoplasty. Preoperatively, the surgeon plans to resect skin, a strip of orbicularis oculi muscle, and a small amount of orbital fat. During the dissection, there is concern that the levator tendon has been lacerated just above the tarsal plate. This can be confirmed by visualizing which of the following structures through the laceration?
(A) Capsulopalpebral fascia
(B) Müller’s muscle
(C) Orbital septum
(D) Retro-orbicularis oculi fat
(E) Whitnall ligament
The correct response is Option B.
Superior to the tarsus, the layers of the eyelid are the conjunctiva, Müller’s muscle, levator tendon, orbital fat, orbital septum, retro-orbicularis oculi fat, orbicularis oculi muscle, and skin. Because the Müller’s muscle lies just below the levator tendon, visualization of this muscle confirms laceration of the tendon.
The conjunctiva is located deep to the Müller’s muscle. In this procedure, the conjunctiva would not be visualized unless the Müller’s muscle had been lacerated also. The orbital septum and retro-orbicularis oculi are anterior and superior to the levator tendon. The Whitnall ligament also is superior to the levator tendon.
A 2-week-old neonate has bilateral prominent ears with lopped superior poles. Which of the following is the most appropriate management?
(A) Observation
(B) Molding the ears using tape and splinting
(C) Injection of a corticosteroid
(D) Otoplasty at age 2 years
(E) Otoplasty at age 6 years
The correct response is Option B.
In this neonate with bilateral prominent ears, immediate management should include molding of the ears with tape and splinting. Circulating maternal estrogens are still present until the age of 6 months, allowing for successful molding of the soft, malleable ear cartilage in infants with cryptotia and prominent ears. Molding can also be performed in newborns with lop ear and Stahl’s ear during the neonatal period. Complete correction without surgery is a realistic expectation.
Because the concept of body image typically begins to form at about school age, ear reconstruction, if required, should ideally be performed between the ages of 5 and 6 years. The normal ear is within 6 to 7 mm of its full vertical height by the age of 6 years, allowing for the construction of an ear that is symmetrical to the normal ear.
Observation alone is inadequate in a child with ear deformities, and injection of a corticosteroid is inappropriate management. Otoplasty should not be performed at the age of 2 years because ear growth is not complete.
A 10-year-old boy presents with an ear injury sustained after a picture frame fell onto his head. The injury is shown in the photograph. He never lost consciousness and has no other injury. Microsurgical reattachment is not an option. Which of the following is the most appropriate initial treatment?
A) Debridement and closure
B) Dressing with petroleum gauze
C) Immediate flap reconstruction
D) Reattach as a composite graft
E) Split-thickness skin graft

The correct response is Option D.
While composite grafting of large ear avulsions has a globally poor outcome, the avulsed fragment in this patient is a thin piece of the helical rim that includes only a small piece of the helical rim cartilage. The shape of the defect, minimal cartilage involvement, and the fact that this was a clean injury in a young patient, makes an initial attempt to replace the tissue as a composite graft the best initial option. At worst, the tissue acts to cover the wound until a definitive reconstruction can be planned. At best, the tissue survives to some degree and salvages some of the delicate and very hard to replace helical rim contour. This patient described in the clinical scenario had 80% survival of the tissue with this technique and required no further reconstruction.
The exposed cartilage is at risk for infection and may dessicate, so a simple dressing change with petroleum is ill advised. Debridement and closure might be possible if more cartilage was removed, but this further compounds the tissue loss. A split-thickness skin graft contracts and may not take well on exposed cartilage. Immediate flap reconstruction is possible, but a flap can always be done at a later time if the composite graft does not survive.
A 2-month-old boy is brought to the office by his parents for consultation regarding congenital lop ear. On the basis of the physical examination, nonoperative correction of the deformity with thermoplastic splinting is planned. The parents ask how long their son will be required to wear the splint. The physician tells the parents that if their son wears the splint as directed, the most likely length of time between application of the device to full correction of the deformity is which of the following?
(A) One week
(B) Two months
(C) Four months
(D) Eight months
(E) One year
The correct response is Option B.
Nonsurgical treatment of various congenital auricular deformities has been reported in children of neonatal age. More recently, this has also been achieved in children who are several years of age. The splints are made from a malleable thermoplastic material and are applied to the ear by hand until a normal form is attained. Remodeling can be performed once per week until a desired correction is achieved. In one study involving 290 patients, 70% of cases could be treated with good results. The average time for treatment was 1.9 months (range, one week to four months). All patients showed remarkable improvement within the first one to two weeks after beginning the treatment. Young age, cooperation of the parents and patient, elasticity of the cartilage, and type of deformity are all contributing factors in the time required for treatment.
A 64-year-old woman is evaluated because of right-sided epiphora. Examination shows the condition of the patient’s eyelids is appropriate for her age. Which of the following is the best diagnostic evaluation to determine if this patient has nasolacrimal duct obstruction?
A) Goldmann tonometry
B) Jones test
C) Optical coherence tomography
D) Seidel test
E) Snap-back test
The correct response is Option B.
The best diagnostic test for nasolacrimal duct obstruction is the Jones test. The Jones I test evaluates lacrimal outflow under normal physiologic conditions. Fluorescein dye is instilled into the conjunctival cornice. The dye is then recovered from the nose after 5 minutes by asking the patient to blow their nose. Absence of dye from the Jones I test could mean a false-negative result, physiologic dysfunction, or anatomic obstruction. A Jones II test is performed following an unsuccessful Jones I test. For the Jones II test, the residual fluorescein is flushed from the conjunctival sac with clear saline. The investigator then asks the patient to expel the drainage from the pharynx and determines the presence or absence of fluorescein in the retrieved saline fluid. Absence of fluorescein indicates a complete nasolacrimal duct obstruction or canalicular obstruction.
The snap-back test is incorrect because it tests horizontal lower eyelid laxity. It is performed by displacing the lower eyelid inferiorly. With normal laxity, it almost immediately snaps back into place against the globe. With increased laxity, the lid will require one or more blinks to resume the normal apposition.
Optical coherence tomography is a noninvasive imaging test that uses light waves to take cross-section pictures of the retina. The Seidel test can detect leaking aqueous or exposed vitreous. Fluorescein ophthalmic strips are wet with normal saline. The fluorescein is dark orange but becomes bright green under blue light when it comes in contact with aqueous.
Goldmann tonometry measures intraocular pressure. A prism mounted on the tonometer head is placed against the cornea. When an area of 3.06 mm has been flattened, the opposing forces of corneal rigidity and the tear film are approximately equal and cancel each other out. The intraocular pressure can then be calculated.
Microtia is an auricular deformity most commonly found in patients with which of the following syndromes?
A) Apert
B) Binder
C) Crouzon
D) Pfeiffer
E) Treacher Collins
Treacher Collins syndrome is characterized by bilateral abnormalities of structures within the first and second branchial arches. Treacher Collins syndrome has anomalies in structures derived from the first branchial arch, groove, and pouch. It is considered to be autosomal dominant in its inheritance with variable expressivity. Features include a convex facial profile with a retrusive lower jaw and chin, down-slant of the palpebral fissures, lower eyelid colobomas, partial absence of eyelid cilia, absent or malformed external ears, hypoplasia of the malar bones, and variable cleft palate.
Binder syndrome is characterized by nasomaxillary hypoplasia. Apert, Crouzon, and Pfeiffer syndromes are all craniosynostotic syndromes that result in mid-facial hypoplasia and a concave facial profile of varying degrees. These syndromes do not typically present with microtia.
Which of the following best describes the main difference between the Nagata and Brent techniques of ear reconstruction for microtia?
A) Nagata is performed at 5 years of age, while Brent is only performed around 12 years of age
B) Nagata is performed in two stages, while Brent is performed in three or more
C) Nagata uses a microvascular omental flap, while Brent only uses local tissue
D) Nagata uses a porous polyethylene framework, while Brent uses autologous cartilage
E) Nagata uses local tissue for framework reconstruction, while Brent uses autologous cartilage and iliac crest bone
The correct response is Option B.
The primary advantage of the Nagata technique is that it typically uses fewer stages than the Brent technique. The principle difference between the two approaches lies in how the lobule and the tragus are reconstructed. In the traditional Brent sequence, lobule creation/elevation and tragal reconstruction are separate stages, while in the Nagata approach, these are created/elevated during the same stage as framework implantation.
Although microvascular techniques may be added as adjunct procedures to a particular approach, they are typically used as a salvage method for a secondary reconstruction if there is framework exposure or loss in either technique.
The Nagata and Brent techniques use autologous rib cartilage for framework reconstruction. Neither technique routinely uses iliac crest bone. The Reinisch technique is a more recently described approach to microtia ear reconstruction and uses a porous polyethylene implant, but the Brent and Nagata techniques have typically used autologous costal cartilage for the framework.
In a child with microtia, growth of the reconstructed ear is primarily dependent on which of the following factors?
(A) Age of the child
(B) Presence of the perichondrium
(C) Preservation of intercostal muscle
(D) Type of fixation
(E) Type of rib graft
The correct response is Option B.
An intact perichondrium is most crucial for growth of the reconstructed ear. If the perichondrium is present, the reconstructed auricular framework will grow at a rate similar to that of the normal ear. The age of the child and timing of reconstruction are secondary considerations because the auricle reaches near normal size at approximately 6 years of age. Preservation of the intercostal muscle attached to the graft does not influence future growth of the reconstructed ear, nor does the type of fixation used. Only rib cartilage should be used for grafting, and bone should not be included.
A 5-year-old girl is brought to the physician because her parents are interested in correction of the unilateral ear anomaly shown in the photographs. Which of the following materials is most likely to be used in the procedure to correct this anomaly?
A) Acellular dermal matrix
B) Autogenous rib cartilage
C) Porous polyethylene
D) Silicone
E) Skin

The correct response is Option E.
This patient has cryptotia. The superior helical rim and scapha are not absent but lie buried under the supra-auricular skin. Although some authors have advocated expanding the superior helical framework, this is rarely indicated. In this patient with very mild auricular shortening, supplementing or reconstructing the cartilage framework with rib cartilage, polyethylene, or silicone is unnecessary. Instead, the ear framework simply released its posterior aspect and the resultant defect lined with full-thickness skin graft or any number of skin flaps raised from the postauricular region. The use of acellular dermal matrix is not an accepted method of correcting cryptotia.

















