Ear Reconstruction - Microtia - Trauma Flashcards
A 7-year-old Asian American boy is brought to the office because of congenital cryptotia. Which of the following is the most likely pathophysiologic explanation for his condition?
A) Abnormal distribution of the intrinsic transverse and oblique auricular muscles
B) Failure of the antihelix to furl during weeks 12 to 16 of gestation
C) Failure of hillocks 3 and 4 to arise from the first and second branchial arches
D) Incomplete fusion of the six hillocks
E) Malformation of the conchal bowl
The correct response is Option A.
Cryptotia is a congenital ear deformity in which the upper pole appears buried beneath the mastoid skin. It is a common auricular malformation in Asians. Children with this condition often present when they are in elementary school, and are unable to wear eyeglasses. The cause of this condition is the abnormal distribution of the intrinsic auricular muscle. Malformation of the conchal bowl results in prominence of the pinna from the head. Incomplete fusion of the six hillocks does not result in cryptotia, nor does it result from failure of the two superior hillocks (3 and 4) to arise from the branchial arches. Failure of the antihelix to furl during weeks 12 to 16 results in a protruding scapha.
A 20-year-old man has severe right ear pain 24 hours after undergoing bilateral otoplasty. Which of the following is the most likely cause?
(A) Chondritis
(B) Excessively tight dressings
(C) Hematoma
(D) Nerve injury
(E) Otitis externa
The correct response is Option C.
Severe unilateral pain in the ear occurring within the first 24 hours after surgery is most consistent with the development of a hematoma resulting from increased pressure on the surrounding soft tissue. If the hematoma is not evacuated urgently, more severe complications, such as pressure necrosis of the overlying skin or underlying cartilage and fibrosis of the soft tissues, may result.
Chondritis, an uncommon complication of otoplasty, is characterized by pain, swelling, and tenderness of the affected ear. This condition initially presents several days after surgery and is best managed with intravenous antibiotic therapy. Surgical exploration is indicated in those patients diagnosed with suppurative chondritis.
Excessively tight dressings and head wraps would be detected soon after surgery, as the effects of the anesthesia dissipate, and would be associated with bilateral pain.
Patients who sustain injuries to the great auricular nerve during otoplasty would experience paresthesia and dysesthesia of the involved ear several weeks following surgery.
Otitis externa would not develop as soon as 24 hours after surgery.
A healthy 7-year-old boy with anotia undergoes reconstruction of the right ear via implantation of a high-density porous polyethylene prosthesis. Compared with use of autologous cartilage, which of the following is the most likely result of this procedure?
(A) Higher incidence of contour deformities
(B) Higher incidence of extrusion
(C) Increased likelihood of malposition
(D) Lower incidence of infection
(E) More resorption of the implant over time
The correct response is Option B.
High density porous polyethylene (Medpor) is an alloplastic implant material that is nonresorbable and highly biocompatible. It has an intramaterial porosity with a pore size between 1 25 and 250 micrometers
which permits extensive fibrovascular ingrowth throughout the implant. Although limited bony ingrowth may occur in select clinical circumstances, the material should not be considered truly osteoconductive. This bony and fibrovascular ingrowth can make this type of material somewhat difficult to remove. Studies have shown less underlying bone resorption occurs with high €‘density polyethylene than with other implant materials. As an alloplastic material, it should not be placed in contaminated wound beds, because it can get easily infected, and should always be positioned in areas of adequate soft tissue cover to prevent extrusion. The incidence of extrusion is higher in microtia reconstruction and nasal dorsum augmentation for this reason.
An 8-year-old girl (shown) is brought to the office because of bilateral microtia. She has severe conductive hearing loss bilaterally. Her middle ear ossicles are fused, and she is not a good candidate for middle ear reconstruction. Reconstruction of the ears using autologous rib cartilage and placement of bone-anchored hearing aids (BAHAs) are planned. Which of the following is the most appropriate time for placement of the BAHAs?
A) Following completion of the ear reconstruction
B) During elevation of the carved-rib framework
C) During placement of the carved-rib framework
D) During rotation of the earlobe
E) Prior to the ear reconstruction
Patients with severe microtia almost invariably have conductive hearing loss resulting from abnormalities of the middle ear. In some patients, the auditory ossicles are sufficiently formed to allow attempted reconstruction of the auditory canal and the middle ear ossicles. Eligibility for this procedure depends upon the development and shape of the auditory ossicles (Jahrsdoerfer grade), as determined by a specialized CT scan of the temporal region. In patients with unilateral microtia and normal contralateral hearing, assistive devices or middle ear reconstruction are rarely indicated and would serve only to improve sound localization. In these patients, protection of hearing in the normal ear is paramount. When bilateral conductive hearing loss is present, methods to improve hearing competence include external hearing aids, bone-anchored hearing aids (BAHAs), and middle ear reconstruction in selected patients. The BAHA is affixed in the mastoid region using an osseointegrated implant. Since this can compromise the integrity and mobility of the skin envelope that will cover the autologous rib cartilage framework, it is often recommended that placement of the BAHA device be deferred until after the ear construction is complete.
A male newborn is evaluated in the hospital because of prominent ears. Nonsurgical correction with auricular molding is recommended. In order to achieve optimal correction, therapy should be initiated at which of the following ages?
A) 3 days
B) 14 days
C) 1 month
D) 6 months
E) 1 year
The correct response is Option A.
If treatment is initiated within the first few days of life, auricular molding can adequately and permanently treat some congenital ear deformities. Treatment must be initiated before 3 days of age and continue to 6 months of age. The efficacy of this mode of treatment is attributed to cartilage pliability due to high concentrations of circulating maternal estrogen in the first few days of life. Maternal estrogen concentrations are highest in the first 3 days of life and begin to decrease thereafter. In order to achieve good results with auricular molding, treatment must be initiated while maternal estrogen concentrations are increased and therefore cartilage pliability is high.
Which of the following structures provides sensation to the upper cranial surface of the ear?
(A) Anterior branch of the great auricular nerve
(B) Arnold’s branch of the vagus nerve
(C) Auriculotemporal nerve
(D) Lesser occipital nerve
(E) Posterior branch of the great auricular nerve
The correct response is Option D.
Branches of the lesser occipital nerve supply sensation to the upper cranial surface of the ear and skin of the anterior and superior surfaces of the external auditory canal. The anterior branch of the great auricular nerve (which forms from branches of cervical nerve roots C2-3 within the cervical plexus) supplies sensation to the lower half of the lateral surface of the ear, while the posterior branch innervates the lower portion of the cranial surface of the ear. The auriculotemporal nerve provides sensation to the anterosuperior surface of the external ear. Arnold’s nerve, which is a branch of the vagus nerve, supplies sensation to the skin of the concha and posterior ear canal.
An otherwise healthy 3-day-old term female infant is brought to the clinic for evaluation of a prominent ear deformity. The parents are interested in nonsurgical options, and they would like to pursue ear molding but are concerned about the complications associated with molding devices. The parents should be advised that the most common complication of such devices is which of the following?
A) Chondritis
B) Otitis media
C) Overcorrection
D) Sensorineural hearing loss
E) Skin ulceration
The correct response is Option E.
Although all of the answers are potential complications of treatment with ear molding, the most common complication is skin ulceration. In a recent study, skin ulceration occurred at a rate of 7.6%. Other studies have reported the rate of skin ulceration around 3%. Although chondritis and allergy to adhesives are complications, their rates were lower than 3 to 7.6%. Since this is an external system, it should not impact eustachian tube dysfunction. Ear molding does not contribute to hearing loss. Overcorrection is not likely with molding alone.
A 22-year-old man comes to the office because he is dissatisfied with the appearance of his ears. Physical examination shows bilateral effacement of the antihelical folds, conchal hypertrophy, and severe prominence of the lobules. Otoplasty is performed with a posterior incision and placement of permanent sutures from the scaphal cartilage and helical sulcus cartilage to the mastoid fascia. Following surgery, the patient is satisfied with the appearance of the upper and middle parts of the ears but notes persistent prominence of the lobules. Which of the following is the most likely cause?
A ) Inadequate reduction of the antitragus
B ) Inadequate reduction of the cavum conchae
C ) Overtightening of the scapha-mastoid sutures
D ) Suturing the triangular fossa to the temporal fascia
The correct response is Option B.
As the cartilage angle between the cavum conchae (conchae) and the antitragus becomes more acute, hypertrophy of the cavum conchae projects the lower third of the ear, forcing the lobule outward. Failure to adequately reduce the cavum conchae before suture placement will lead to persistent prominence of the lobule.
The antitragus and lobule are not directly excised during standard otoplasty. Overtightening of the scapha-mastoid sutures leads to a ‘pinned-back’ appearance. Suturing the triangular fossa to the temporal fascia corrects prominence of the upper ear.
Each of the following deformities is commonly associated with microtia EXCEPT
(A) cervical spine abnormalities
(B) inner ear abnormalities
(C) macrostomia
(D) mandibular hypoplasia
(E) preauricular pits
The correct response is Option B.
Patients with microtia have partial or complete absence of the external ear structures due to abnormal embryologic development of portions of the first, or mandibular, and second, or hyoid, branchial arches. This typically occurs during the fourth to twelfth week of intrauterine development and affects the auditory ossicles, external auditory canal, middle ear cavity, and tympanic membrane. Several abnormalities can occur in conjunction with microtia. Orbital auricular vertebral syndrome, also known as Goldenhar syndrome, and the Tessier No. 7 cleft also result from abnormalities in the development of the first and second branchial arches. Orbital auricular vertebral syndrome is characterized by microtia, cervical spine abnormalities, mandibular hypoplasia, preauricular pits and sinuses, and hemifacial microsomia. The Tessier No. 7 cleft manifests as microtia, macrostomia, and preauricular sinuses.
Because the external auditory meatus and internal ear are derived from different structures, the internal ear is usually well constructed in patients with microtia. Likewise, patients with orbital auricular vertebral syndrome have abnormalities of the middle and external ear but not the inner ear.
Six months after undergoing bilateral otoplasty for correction of prominent ears, a 27-year-old man has recurrent prominence of the upper half of the left ear. At follow-up examination one month after surgery, the ears appeared symmetric.
Which of the following is the most likely cause of this patient’s recurrent deformity?
(A) Disruption of the conchal-mastoid sutures
(B) Disruption of the sutures used to create the antihelical fold
(C) Inadequate excision of cartilage from the concha
(D) Inadequate excision of skin from the posterior ear
(E) Incorrect placement of the postoperative dressing
The correct response is Option B.
The most likely cause of this patient’s recurrent prominence of the upper half of the left ear is inadequate placement of sutures used in the creation of the antihelical fold. Lack of formation of the antihelical fold is one of the most common causes of prominent ears. Surgical creation of the fold can be accomplished with permanent sutures alone, cartilage incision or resection combined with sutures, or abrasion of the lateral ear cartilage with or without sutures. When used alone, sutures are usually very effective in the creation of the antihelical fold in children because their ear cartilage is soft and pliable. In adults, who have less pliable cartilage, sutures can be used alone to create a fold, but frequently other techniques must be performed to allow the cartilage to bend. When sutures are used alone, they must be permanent and precisely placed, or relapse can occur.
Excision of conchal cartilage, skin resection, placement of conchal-mastoid sutures, and placement of the postoperative dressing, while all vital aspects of otoplasty for prominent ears, are less likely to be involved in recurrence of the deformity than the inadequate creation of the antihelical fold, which is most commonly associated with recurrence of the deformity.
A 25-year-old woman has facial asymmetry. She says that she has had progressive loss of soft-tissue volume on the right side of the face since age 10 years that became stabilized four years ago. Examination shows significant subcutaneous atrophy of the right side of the face without bony asymmetry. She also has hypopigmentation of the iris on the affected side.
Which of the following is the most appropriate management?
(A) Bone graft augmentation of the midface
(B) Alloplastic augmentation
(C) Reconstruction with a microvascular serratus anterior free flap
(D) Reconstruction with a microvascular parascapular free flap
(E) Reconstruction with a superficial temporal fascia flap
The correct response is Option D.
This 25-year-old woman has Romberg’s hemifacial atrophy characterized by progressive unilateral loss of facial soft tissue. The underlying skeleton is also affected in patients with severe forms of the disease. Surgery should be delayed until the condition becomes stabilized, which is indicated by the cessation of facial atrophy. When this has occurred, a microvascular parascapular flap can be deepithelialized and customized to fit the dimensions of the defect, and then transferred and buried subcutaneously.
Skeletal augmentation with either bone graft or alloplast is not appropriate because the bones of the face are not affected. The serratus anterior flap would only atrophy over time, and the superficial temporal fascia flap would not provide the necessary volume.
A 2-week-old female infant is evaluated because of a prominent ear deformity. Which of the following is the most appropriate early management to address this deformity?
A) Cartilage grafting
B) External molding
C) Injection of hyaluronidase
D) Otoplasty
E) No intervention at this time
The correct response is Option B.
External molding is the early treatment of choice for a prominent ear deformity. Ideally, this is started by 2 weeks of age, but improvement has been seen in patients up to 3 months of age and is worth trying. Splinting is a shorter therapy used for Lop ear and Stahl ear deformation. Injectable chondroplasty using hyaluronidase is still in the trial phase, but if effective, would allow molding to be used in children older than 3 months of age. Otoplasty at 6 years of age is the alternative if molding therapy is unsuccessful.
Which of the following congenital ear deformities is characterized by absence of the superior auriculocephalic sulcus?
(A) Cryptotia
(B) Cup ear deformity
(C) Lop ear
(D) Microtia
(E) Prominent ear deformity
The correct response is Option A.
Cryptotia (“hidden ear”) is a congenital deformity of the cartilage of the scapha and antihelix. In neonates who have this deformity, the upper pole of the ear is buried beneath the scalp, and the superior auriculocephalic sulcus is absent. Conservative management is most appropriate initially; surgical release should be performed when the child is older.
Infants with the cup ear deformity have hooding of the scapha and helix and flattening of the antihelix. Lop ear is characterized by protrusion of the ear and folding of the superior helix. Microtia is a hypoplastic condition that manifests as varying degrees of ear absence, from anotia (complete ear absence) to a smaller than normal ear with normal morphology. The prominent ear deformity involves widening of the conchoscaphal angle, increased auriculocephalic distance, and loss of the antihelical fold.
A 21-year-old man sustains a complete amputation of the right ear at the level of the external auditory canal in a motor vehicle collision. There are no other injuries. Which of the following procedures will provide the best aesthetic result?
(A) Delayed total ear reconstruction with a rib cartilage graft
(B) Dermabrasion of the epidermis of the amputated ear, burial of the ear in a subcutaneous postauricular pocket, followed by removal and coverage with a skin graft or flap
(C) Removal of the skin of the amputated ear, reattachment of the ear cartilage, and immediate coverage with a temporoparietal fascial flap and skin graft
(D) Composite grafting of the amputated ear followed by surface cooling
(E) Microsurgical ear replantation
The correct response is Option E.
Successful microsurgical replantation of the ear provides superior aesthetic results while eliminating the need for other complex reconstructive procedures. However, this technique is associated with increased operative time and the need for multiple blood transfusions. Hospitalization is typically prolonged, and failure rates associated with the procedure are high.
Delayed reconstruction results in only moderate cosmetic improvement, and secondary reconstruction does not sufficiently recreate the intricate architecture of the external ear.
Primary nonvascularized replantation of the ear produces a good appearance initially because of the survival of the avulsed cartilage; however, late distortion of the cartilage frequently limits the overall aesthetic result. Techniques used for nonvascularized replantation include primary reattachment of the ear with surface cooling, dermabrasion of the ear, and partial or complete burial of the ear in a postauricular skin pocket, followed by coverage of the filleted cartilage with a temporoparietal fascial flap and skin graft.
A 10-year-old boy presents with an ear injury sustained after a picture frame fell onto his head. The injury is shown in the photograph. He never lost consciousness and has no other injury. Microsurgical reattachment is not an option. Which of the following is the most appropriate initial treatment?
A) Debridement and closure
B) Dressing with petroleum gauze
C) Immediate flap reconstruction
D) Reattach as a composite graft
E) Split-thickness skin graft
The correct response is Option D.
While composite grafting of large ear avulsions has a globally poor outcome, the avulsed fragment in this patient is a thin piece of the helical rim that includes only a small piece of the helical rim cartilage. The shape of the defect, minimal cartilage involvement, and the fact that this was a clean injury in a young patient, makes an initial attempt to replace the tissue as a composite graft the best initial option. At worst, the tissue acts to cover the wound until a definitive reconstruction can be planned. At best, the tissue survives to some degree and salvages some of the delicate and very hard to replace helical rim contour. This patient described in the clinical scenario had 80% survival of the tissue with this technique and required no further reconstruction.
The exposed cartilage is at risk for infection and may dessicate, so a simple dressing change with petroleum is ill advised. Debridement and closure might be possible if more cartilage was removed, but this further compounds the tissue loss. A split-thickness skin graft contracts and may not take well on exposed cartilage. Immediate flap reconstruction is possible, but a flap can always be done at a later time if the composite graft does not survive.
A 6-year-old girl with prominent ears due to overdeveloped conchae and effaced antihelical folds is scheduled to undergo otoplasty by a combination of methods including Stenstrom cartilage abrasion. In this technique, which of the following surfaces of the auricular cartilage is abraded?
(A) Anterior surface of the antihelix
(B) Anterior surface of the conchal bowl
(C) Lateral border of the helix
(D) Posterior surface of the antihelix
(E) Posterior surface of the conchal bowl
The correct response is Option A.
Classic congenital prominence of the ears is caused by an overdeveloped or excessively deep conchal bowl; an underdeveloped, effaced, or absent antihelical fold; or both. Surgical correction of prominent ears commonly calls for a combination of procedures, including the Mustardé technique for placement of mattress sutures to create an antihelical fold, partial excision of the conchal bowl, placement of concha-mastoid sutures for setback of the conchal bowl, and Stenstrom cartilage abrasion.
Stenstrom cartilage abrasion requires partial thickness scoring, scratching, or abrading of the anterior surface of the antihelix. This causes the cartilage to bend away from the abraded surface, creating or accentuating an antihelical fold.
To correct prominent ears, projection of the conchal bowl usually needs to be reduced by excision or by setback with placement of concha-mastoid sutures, not by scoring the anterior or posterior surface. Because the helix is normal in prominent ears, it should not be abraded.
An otherwise healthy 2-week-old male newborn is brought to the office because his parents are concerned about the appearance of his right ear. Physical examination shows a folded upper helix. All components of the auricular structure are present. Gentle digital manipulation restores the ear to normal shape. Which of the following is the most appropriate initial management?
A) Application of a conforming splint
B) Burying of the helical cartilage in a retroauricular pocket
C) Rasping of the antihelical fold with an otoabrader
D) Resection of the superior auricular muscle
E) Surgical repair with cartilage grafts
The correct response is Option A.
Lop ear is among the deformations that are acquired in utero, as opposed to true congenital malformations, in which elements of the auricle may be underdeveloped or missing altogether. Circulating maternal estrogens are thought to be the cause of the softened cartilage, which lacks sufficient stiffness to support the upper helix. The cartilage should respond to shaping with a splint that is formed to match the contour of the normal helix. The splint is applied for several weeks or more. The other options involving surgical management are not indicated as primary therapy in the patient described. Resection of the superior auricular muscle may increase the superior auriculocephalic distance and aggravate the malposition of the upper helix. Cartilage rasping is indicated for the treatment of prominent ears in an older child to create a normal antihelical fold. Burying the helical cartilage beneath the mastoid skin is indicated for management of soft-tissue avulsion injury as a prelude to reconstruction. Surgical repair with cartilage grafts is unnecessary.
A 21-year-old man comes to the office for consultation because he thinks his ears protrude. He appears self-conscious about his ears and wears his hair long to hide them. He repeatedly looks in the mirror during his evaluation. On examination, postauricular measurement shows a helical rim-to-head distance of 12 mm at the superior pole, 17 mm at the midpoint, and 23 mm at the lobule bilaterally. Which of the following is the most appropriate next step in management?
A ) Referral for psychological evaluation
B ) Re-evaluation in 1 year
C ) Resection of the conchal bowl
D ) Scoring of the anterior cartilage
E ) Conchal-mastoid suturing
The correct response is Option A.
The patient described exhibits traits consistent with body dysmorphic disorder (BDD). DSM-IV describes BDD as a preoccupation with an appearance that is either imagined or is a slight physical anomaly. The preoccupation must cause clinically significant distress or impairment in social, occupational, or other important areas of functioning. The degrees of emotional distress and behavioral impairment, rather than the size or nature of the physical defect, may be more accurate indicators. Although possibly more difficult to diagnose in the cosmetic surgery patient population, plastic surgeons should evaluate for possible underlying psychiatric disorders. Psychiatric illnesses are not absolute contraindications for surgery; however, cosmetic surgery is unlikely to benefit those with BDD, psychoses, or eating disorders.
Normal helical rim-to-head measurements for each third of the ear are 10 to 12 mm at the helical apex, 16 to 18 mm at the midpoint, and 20 to 22 mm at the lobule.
A 2-month-old female infant is evaluated for the ear anomaly shown in the photograph. Which of the following most accurately describes the anomaly?
A) Anotia
B) Crumple ear
C) Cryptotia
D) Lop ear
E) Stahl ear
The correct response is Option C.
This is cryptotia, a deformity of the ear in which the superior helical rim is buried beneath the skin of the scalp. Some studies report successful treatment with early ear molding, but this often requires elevation of the helical rim and application of a skin graft or regional flap to line the posterior aspect.
Anotia refers to complete absence of the ear structures, while lop ear is an ear that is typically constricted and has an overhang or hooding of the superior helical rim. Crumple ear is a form of constricted ear with variable cartilage abnormalities that give it an irregular appearance. Lastly, Stahl ear refers to an otherwise normal-sized ear with a third crus, usually accompanied by an evagination of the helical rim.
A 50-year-old man is brought to the emergency department 90 minutes after he sustained injuries in a motor vehicle collision. Physical examination shows a severe abrasion injury to the right ear with partial degloving of the superior helical rim extending into the concha. The skin over the upper third of the ear is missing at variable depths. Which of the following is the most appropriate initial step in management?
(A) Conservative debridement and topical wound care
(B) Debridement and coverage with a local flap
(C) Debridement and skin grafting
(D) Debridement, coverage with a temporoparietal fascia flap, and skin grafting
(E) Resection and primary wound closure
The correct response is Option A.
The patient described has a partial-thickness injury involving the upper third of the ear. It is often not clear initially if the perichondrium is viable in this situation. Although the patient may require coverage of the exposed cartilage with a flap, initial management is most often conservative. The most appropriate initial step is conservative debridement and topical wound care including dressing changes until the devitalized tissues demarcate. This management allows for a full assessment of the extent of the injury. It is important that the dressings prevent desiccation and infection of the exposed perichondrium.
Debridement followed by immediate skin grafting is not appropriate because skin graft take is often unreliable if the cartilage is exposed. Also, the extent of tissue injury caused by shearing and blunt trauma is difficult to assess initially because of the soiled and edematous tissues of the fresh trauma.
Debridement, coverage with a temporoparietal fascia flap, and skin grafting is effective in providing a bed for skin grafting but is not the most appropriate initial step in management.
Resection and closure of a defect of this size can be performed, often with an Antia €‘Buch flap after wedge resection with a pentagonal design. However, this procedure will reduce the size of the ear and, therefore, is not appropriate.
A 6-year-old boy with microtia is evaluated for single-staged alloplastic reconstruction. In addition to the prosthesis itself, discussing with the parents soft-tissue reconstruction should focus on tissues dependent on which of the following vasculature?
A) Facial
B) Occipital
C) Submental
D) Superficial temporal
E) Supraorbital
The correct response is Option D.
Although alloplastic reconstruction can be successfully performed in a single stage, 3D printed, and still allow for atresia repair, there is still a soft-tissue component that needs to be addressed. In general, the superficial temporal/temporoparietal fascia flap is the work-horse flap and is based on the superficial temporal vasculature. This requires incisions into the hair-bearing scalp; alopecia and irregular parting of the hair are possible negative outcomes. Additional skin grafting must also be discussed. The other vasculature listed is not directly important for this type of surgery.
A 24-year-old man has pain and swelling of the left ear after injuring the ear in a fight. Physical examination shows obliteration of the normal contours of the lateral surface of the ear. Which of the following is the most appropriate management?
(A) Application of a pressure dressing for several days, followed by evacuation of clotted blood
(B) Needle aspiration of the ear
(C) Needle aspiration of the ear and application of a pressure dressing
(D) Incision and drainage of the skin and perichondrium and application of a pressure dressing
(E) Excision of thickened tissue and placement of suction-drainage catheters
The correct response is Option D.
Hematoma formation is the primary complication of blunt trauma to the ear. The mechanism of injury involves disruption of blood vessels in the perichondrium, leading to hemorrhage. The blood fills the space between the perichondrium and cartilage, distorting the contour of the lateral ear into a convex shape and blocking the vascular supply to the cartilage, which is derived from the perichondrium. Necrosis or infection of the cartilage results.
Prompt treatment involves removing the accumulated blood while maintaining pressure on the affected area for several days to prevent recurrence. To accomplish this, an incision is made through the skin and perichondrium on the inner side of and parallel to the antihelix, which will conceal the scar. The blood is drained and the wound is inspected for further bleeding. When the surgeon is assured that the bleeding has stopped, a pressure dressing and a head dressing are applied.
Late treatment of a cauliflower ear deformity involves excision of the thickened tissue, including fibrous tissue and new cartilage, followed by application of a pressure dressing.
Simple needle aspiration of the blood is likely to result in development of seroma.
An 89-year-old man presents with a 5 x 5-cm ulcerated, biopsy-proven squamous cell carcinoma of the skin involving the pinna of the right ear. On examination, no palpable adenopathy is noted. Radiation Therapy (RT) is planned. Which of the following is the primary predictor of local control rates of RT in this patient?
A) Age of patient
B) Histology of tumor
C) Location of tumor
D) Presence of ulceration
E) Size of tumor
The correct response is Option E.
The National Comprehensive Cancer Network (NCCN) has published guidelines for radiation therapy for primary squamous cell carcinoma (SCC). Local control rates for SCCs less than 1 cm were 91%; those 1 to 5 cm were 76%, those larger than 5 cm were 56%.
Mohs micrographic surgery has the highest reported cure rates for SCC compared with all other modalities. However, these rates begin to drop with increased tumor size, differentiation, discontinuity, perineural invasion, and history of recurrence.
Of the head and neck sites, involvement of the ears and lips confers the highest risk for metastatic disease at 8.8% and 13.7%, respectively. In tumors greater than 2 cm in size, the risk may increase.
In the past, it was felt that lesions overlying cartilage should not be treated with radiation therapy due to the risk of chondronecrosis. It is now known that such sites can be safely treated with fractionated radiation therapy.
Radiation therapy for regional node involvement should be considered. NCCN guidelines suggest 25 (2Gy) fractions to clinically negative but “at risk” nodal basins over a 5-week period.
Age, tumor location, ulceration, and histology are secondary predictors to tumor size.
A 28-year-old man comes to the office because of fever and increasing pain 1 week after partial amputation of the right ear when he was bitten during a fight. The wound was irrigated and repaired in the emergency department. Temperature is 100.4 °F (38.0 °C). Examination shows erythema and swelling of the entire ear and a small area of dehiscence containing pus along the posterior suture line. Which of the following is the most important step in management?
A ) Application of wet-to-dry dressings
B ) Completion of the amputation with sparing of cartilage in a remote subdermal pocket
C ) Intravenous antibiotic therapy
D ) Irrigation, debridement, and packing the wound open
E ) Oral antibiotic therapy
The correct response is Option D.
Auricular chondritis and perichondritis is a serious surgical infection requiring immediate surgical intervention as the primary course of treatment in traumatic cases. Culture swabs should also be obtained and will guide antibiotic therapy for associated cellulitis; however, broad spectrum coverage initially is appropriate. Chondritis complicating elective otoplasty is sometimes handled in a more stepwise approach, sometimes initiating intravenous antibiotics while removing a few sutures to allow drainage and/or insertion of a small irrigating catheter. Without a reasonable response in these cases, then standard open irrigation and debridement are done with removal of all sutures, and repeat otoplasty correction is deferred until several months after resolution of the infection.
Antibiotics alone, orally or intravenously, for localized suppurative chondritis are likely to be ineffective without surgical treatment. Likewise, topical dressings without formal opening of the suture line for wide exposure and drainage of the infected cartilage would also be ineffective.
Completing the amputation when the tissues still appear viable is overaggressive at this stage. If and when the majority of the tissue appears unable to sustain sufficient circulation to support its viability, then discarding precious tissue is justified. Salvaging the cartilage framework component in a remote subdermal pocket may be useful; however, the cartilage is infected in this scenario and would require caution, including thorough debridement and lavage with antibiotic solution and close monitoring of the bank.
The ear lobule is innervated by which of the following nerves?
(A) Auriculotemporal
(B) Great auricular
(C) Greater occipital
(D) Lesser occipital
(E) Vagus
The correct response is Option B.
The ear is innervated by multiple nerves. The greater auricular nerve is a branch of C2 and C3. It travels on the superficial surface of the sternocleidomastoid muscle and enters the lower, posterior surface of the ear. Its branches supply the lobule as well as the helix, antihelix, and most of the cranial surface of the ear.
The auriculotemporal nerve is a branch of the third division of the trigeminal nerve and enters the ear near the tragus. It supplies the tragus and the root of the helix. The greater occipital nerve, which is a branch of C2 and C3, supplies the posterior scalp. The lesser occipital nerve is also a branch of C2. It sends off an auricular branch that supplies the upper third of the cranial surface of the ear. The vagus (X) nerve supplies the concha, via its branch called Arnold’s nerve.
A 17-year-old high school wrestler had the sudden onset of swelling of the right ear 24 hours ago. Initial attempts at aspiration of the ear were unsuccessful. On current physical examination, there is a hematoma involving the upper half of the right ear.
Which of the following is the most appropriate management?
(A) Placement of an ice pack on the ear followed by observation
(B) Aspiration of the hematoma after liquefaction
(C) MRI of the ear for delineation of the cartilage fracture followed by surgical repair
(D) Surgical drainage of the hematoma followed by placement of through-and-through sutures with gauze bolsters
(E) Debridement of the skin over the hematoma followed by insertion of the ear cartilage into a postauricular skin flap
The correct response is Option D.
Separation of the skin of the external ear from the cartilage, and the subsequent development of a hematoma because of a shearing type injury, is a known injury in wrestlers and boxers. If not treated correctly it can result in a chronically scarred ear with no definition, commonly referred to as “cauliflower ear.”
Appropriate management of the acute hematoma in this patient is surgical drainage and placement of through-and-through sutures with gauze bolsters to coapt the separated skin to the underlying cartilage. These bolsters are left in place for seven to 10 days. Drainage and suturing can be accomplished under local anesthesia if the patient is cooperative; this procedure will typically allow the skin of the avulsed ear to adhere to the underlying cartilage and prevent the development of the deformity described previously.
Placement of an ice pack followed by observation would only delay appropriate treatment of this patient’s injury. Waiting for the hematoma to liquefy and then aspirating it will not prevent chronic scarring because the skin of the avulsed ear will not adhere correctly to the delicate cartilage framework. An MRI is not necessary and will only delay the appropriate treatment. Debridement of the viable ear skin would be contraindicated because it would only complicate the injury and its management.
A 22-year-old man who is a professional boxer comes to the emergency department because he has a hematoma on the anterior surface of the left ear one hour after he sustained a direct blow to the ear during a match. Which of the following is the most appropriate management?
(A) Application of pressure and ice to the ear
(B) Application of a mold to the ear
(C) Percutaneous drainage of the hematoma
(D) Open drainage of the hematoma and application of a bolster dressing
(E) Open drainage of the hematoma and reshaping of the cartilage
The correct response is Option D.
Auricular hematomas are common in athletes, such as wrestlers and boxers, in whom direct trauma to the ear is possible. Untreated subperichondrial hematomas can lead to formation of new cartilage and the appearance of a thickened and deformed ear (cauliflower ear). To maintain the natural contour of the ear, appropriate management consists of open drainage of the hematoma followed by closure of the incision and application of a tie-over bolster dressing. Percutaneous drainage techniques or simple cold compresses are generally not adequate in completely removing the hematoma. Molds can be used to shape the ear of an infant but not of an adult. Cartilage reshaping techniques, such as scoring, are not necessary in the management of acute auricular hematomas but may be needed for later reconstruction of cauliflower ear.
A 15-year-old boy undergoes reconstruction of a 15-mm2 traumatic defect of the right ear with a graft harvested from the contralateral ear. On examination two days after the procedure, the graft appears dusky. A photograph is shown above. Which of the following is the most appropriate next step in management?
(A) Hyperbaric oxygen therapy
(B) Application of leeches
(C) Release of the sutures
(D) Debridement of the graft
The correct response is Option A.
In this 15-year-old boy who exhibits duskiness at the graft site two days after undergoing composite grafting of the ear, the most appropriate next step is initiation of hyperbaric oxygen therapy. This will provide oxygenation during the critical ischemia period for the graft and thus is likely to improve the outcome. Hyperbaric oxygen therapy enhances antimicrobial activity by facilitating the oxidative burst of polymorphonuclear neutrophils. It increases the hyperoxygenation of tissue to a level that is 10 to 15 times greater than normal. In addition, it stimulates angiogenesis and blunts the ischemia-reperfusion injury response.
Application of leeches is appropriate if arterial input is adequate but venous outflow is insufficient, as in patients undergoing microsurgical replantation who demonstrate thrombosis of the vein, or if a suitable vein does not exist for anastomosis. However, duskiness of the ear is an indication of arterial insufficiency, and leeches would fail to attach if they were applied.
Because a composite graft receives its vascularity through diffusion from the surrounding wound bed, releasing the sutures would inhibit the “take” of the graft to the bed. Similarly, performing debridement two days after grafting is excessive. Instead, the composite graft should be left in place for a minimum of two weeks in order to demonstrate healing and incorporation, as long as infection does not develop.
Which of the following is the most appropriate management of a 1-year-old boy who has isolated microtia on the left?
(A) Fabrication of a costal cartilage framework at age 3 years
(B) Implantation of a Silastic framework at age 4 years
(C) Placement of a bone-conduction hearing aid at age 5 years
(D) Creation of an ipsilateral ear canal at age 6 years
(E) Autologous ear reconstruction at age 7 years
The correct response is Option E.
Although the recommended age of surgery may vary among individual patients with microtia, autologous ear reconstruction is typically performed once the child reaches 5 years of age; most children are between the ages of 6 and 7 years at the time of surgery, at which time there is typically sufficient rib cartilage for reconstruction. The ear attains 85% of its total growth by age 3 years and has almost fully developed by ages 5 to 7 years; however, minimal changes in the width of the ear and its distance from the scalp can be seen until age 10 years.
Hearing in the affected ear should be assessed as soon as possible. When necessary, a bone-conduction hearing aid, whether external or implantable, should be initially used by age 1 year.
Implantation of a Silastic framework is not the first choice for management of congenital microtia. Creation of an ear canal is typically performed for unilateral microtia when the patient is age 13 to 19 years and should not be initiated until reconstruction of the external auricle has been completed.
A 6-year-old boy is undergoing the first stage of total auricular reconstruction for correction of microtia. A finely detailed rib cartilage construct is carved. Which of the following aspects of this patient’s postoperative care should be most effective in safely promoting adherence of the new cartilage construct to the skin cover?
A) Application of cold compresses
B) Application of pressure dressings
C) Closed suction drainage
D) Conforming splinting
E) Open drainage incisions
Attentive postoperative management is imperative in total auricular reconstruction. Skin coaptation to the carved cartilage construct is best provided by continuous closed suction drainage for the first five postoperative days. The reported complication rate is less than 1%. The quantity and quality of drainage can be monitored, and any potential hematoma is removed before it obscures the framework details. This can also be used to aid flap coaptation in cases in which temporoparietal or omental flap coverage is needed. Cold compresses are not effective in promoting adherence of the skin flap to the underlying framework.
Pressure dressings risk skin necrosis over the new cartilage framework and are not preferred over closed suction drainage. One author experienced a 33% skin necrosis complication rate in the first 15 cases in which bolster sutures were used to secure pressure bandages. In some techniques, carefully placed bolster sutures have been advocated to prevent hematoma, although the risk of skin necrosis remains. Additional skin incisions may adversely affect the final result and may also compromise the skin flap.
A 25-year-old man has congestion of the right ear 10 hours after he underwent replantation of the auricle due to near-total amputation of the ear in a motor vehicle collision. During microscopic surgery, a single small artery was anastomosed to relocated superficial temporal vessels. No vein could be located. Which of the following is the most appropriate management of this patient’s current symptom?
(A) Elevation of the head
(B) Topical application of nitroglycerin
(C) Leech therapy
(D) Vein grafting
(E) Surgical reexploration
The correct response is Option C.
Microsurgical ear replantation provides another option in select cases of ear amputation, providing the potential for an unsurpassed aesthetic result. In those relatively few cases in which it is attempted, the small size of the vessel and the component of avulsion can make primary repair of the vessels difficult. Venous congestion occurs to some extent in nearly every case and is the most common cause of postreplantation complications. There have been several case reports of successful ear replantation without a venous anastomosis, although venous anastomosis is recommended whenever possible. Despite this, postoperative congestion can be managed with leech therapy for vascular compromise. Arterial compromise demands reexploration, whereas venous compromise can be managed nonoperatively. Topical vasodilators, such as nitroglycerin, are not recommended for venous congestion. Efforts should be made to improve outflow; therefore, conservative management is not recommended. Elevating the patient=s head may be useful but does not replace the proven effectiveness of leeches and heparin in clear cases of congestion.
A 5-year-old boy presents to the office for evaluation of ear deformity. Examination shows an abnormal bar of cartilage, extending from the antihelix to the helix at approximately the junction between the upper and middle thirds of the ear. Which of the following is the most likely diagnosis?
A) Constricted ear
B) Cryptotia
C) Microtia
D) Question mark ear
E) Stahl ear
The correct response is Option E.
In Stahl ear, there is an abnormal bar of cartilage (sometimes called the third crus), extending from the antihelix to the helix at approximately the junction between the upper and middle thirds of the ear. If that abnormal cartilage is obvious, it must be excised.
In a constricted ear, the fundamental abnormality is that the helical rim is deficient in circumference for the scapha to which it is attached. The inadequate length of the helix “constricts” the ear and forces it into a cupped shape that protrudes from the head.
In cryptotia, the superior aspect of the ear is hidden beneath the temporal scalp. In some cases, the auricular cartilage is normal and requires only to be extracted from its hiding place. Lateral traction on the ear will reveal a normal auricle.
In the question mark ear, there is excess scapha in the upper portion of the ear and a deficiency at the junction of the middle and lower thirds, resulting in a “question mark” shape.
Microtia is a congenital condition in which the cartilage of the outer ear is underdeveloped or absent.
A 7-year-old girl is evaluated because of the ear anomaly shown. CT scan of the temporal bone of the affected ear shows an absent stapes and incus. Construction using autogenous rib cartilage is planned. The girl’s family inquires about options for improving hearing to the affected ear. Which of the following is the most appropriate response?
A) Atresia repair should be performed after auricular reconstruction
B) Atresia repair should be performed before auricular reconstruction
C) A bone-anchored hearing aid should be placed after auricular reconstruction
D) A bone-anchored hearing aid should be placed before auricular reconstruction
E) Hearing cannot be improved in this patient
The correct response is Option C.
Staged autogenous cartilage reconstruction remains the gold standard to correct microtia. The urgency and method of treatment for associated hearing loss depends on whether the problem is unilateral or bilateral, whether external ear construction is planned, and the condition of the middle ear structures. Bilateral hearing loss can result in problems with language development and learning and requires early intervention to improve or restore hearing. This is usually done with external hearing aids in early childhood followed by atresia repair or a bone-anchored hearing aid (BAHA) later in life. Historically, most authorities have concluded that patients with congenital unilateral hearing loss naturally adjust and experience few functional implications. Consequently, most do not routinely recommend operative correction for unilateral hearing loss. There are some recent reports of improved language This examination contains test materials that are owned and copyrighted by the American Society of Plastic Surgeons. Any reproduction of these materials or any part of them, through any means, including but not limited to, copying or printing electronic files, reconstruction through memorization or dictation, and/or dissemination of these materials or any part of them is strictly prohibited. Keep printed materials in a secure location when you are not reviewing them and discard them in a secure manner, such as shredding, when you have completed the examination. Page 249 of 426 development after early biaural hearing restoration, and some clinicians now support early treatment. If correction is considered, the two primary options are atresia repair, wherein the canal is opened and the middle ear is reconstructed, or use of a hearing aid. Atresia repair is usually deferred until the external ear framework is placed or the reconstruction is complete. The success depends on the presence and normalcy of the middle ear structures. Jahrsdoerfer’s 10-point scoring system (10 being most suitable for reconstruction) grades the anatomic appearance and relationship of the middle ear structures by temporal CT scan. Middle ear reconstruction is contraindicated for a score of 5 or less. Based on the information provided, this patient with anotia (-1 point), absence of the stapes (-2 points) and absence of the incus (-2 points), has a maximum score of 5 and would not be a good candidate for middle ear reconstruction. Certainly, this procedure would not improve hearing as well as a hearing aid such as the BAHA. BAHA uses osseointegrated implants to affix a hearing aid. This provides excellent correction of conductive hearing loss and is widely used. BAHA is the best surgical option to restore hearing in this patient if so desired. However, placement should be deferred until after the autologous ear reconstruction is completed.
A 25-year-old man sustained a laceration to the face from a knife in an altercation 1 year ago. He did not receive treatment at the time of injury and now has complete left unilateral facial nerve transection and paralysis. Placement of an upper eyelid gold weight is necessary for eye protection. Which of the following is the appropriate location for placement of the weight?
A) Between the tarsal plate and conjunctiva
B) Centered over the junction of the central and lateral one-third of the eyelid
C) Deep to the levator aponeurosis and superficial to the tarsal plate
D) Immediately superior to the tarsal plate
E) Superficial to the levator aponeurosis and tarsal plate
The correct response is Option E.
The appropriate location for placement of an upper eyelid gold weight is superficial to the levator aponeurosis and tarsal plate, with the inferior edge of the gold weight within a few millimeters of the lash line. It is placed centered over the junction of the medial and central one-thirds of the eyelid and medial limbus.
Lagopthalmos, or the inability to completely close the eyelids, is a common problem after facial nerve transection. The most common surgical treatment modality of lagopthalmos is placement of an upper eyelid gold or platinum plate to weigh down the upper eyelid, allowing for complete eyelid closure, precluding dessication and corneal damage.
A 2-week-old female infant is evaluated because of a prominent ear deformity. Which of the following is the most appropriate early management to address this deformity?
A) Cartilage grafting
B) External molding
C) Injection of hyaluronidase
D) Otoplasty
E) No intervention at this time
The correct response is Option B.
External molding is the early treatment of choice for a prominent ear deformity. Ideally, this is started by 2 weeks of age, but improvement has been seen in patients up to 3 months of age and is worth trying. Splinting is a shorter therapy used for Lop ear and Stahl ear deformation. Injectable chondroplasty using hyaluronidase is still in the trial phase, but if effective, would allow molding to be used in children older than 3 months of age. Otoplasty at 6 years of age is the alternative if molding therapy is unsuccessful.
A 24-year-old man who sustained total amputation of the left ear during an explosion three months ago comes to the office for consultation regarding reconstruction of the ear. Physical examination shows loss of the auricle and tragus with scarring of the skin and scalp surrounding the external auditory canal. Which of the following materials is most appropriate for the first stage of the reconstruction of this patient €™s ear?
(A) Full-thickness skin grafting to replace the scar and subsequent expansion
(B) Radial forearm flap and Silastic framework
(C) Temporalis muscle turnover flap and rib framework
(D) Temporoparietal flap and rib graft framework
(E) Tissue expansion of retroauricular skin and Medpor framework
The correct response is Option D.
The goal of reconstruction of the ear is to restore the cosmesis of the auricle and the function of the superior helical rim in providing support for eyeglasses. Total reconstruction of the ear most likely requires two to three stages. The first stage typically involves creating a cartilage framework and placing it under vascularized tissue. In the scenario described, an ipsilateral temporoparietal fascia pedicled flap or a contralateral free temporoparietal fascia flap (TPFF) covered with a split-thickness skin graft (STSG) is most appropriate. STSGs are generally used because they will shrink and form fit to the auricular cartilage over the TPFF or in the posterior auricular skin crease.
Other options include a local tissue flap or a pre €‘expanded local tissue flap. A tissue expander can be placed and may be appropriate for some patients. However, it is not likely to be successful in the patient described because of the scarred skin in the region of expander placement. A second surgery is usually necessary to recreate the posterior auricular crease and the tragus or lobule. In young patients, rib cartilage is the most common first choice for autogenous framework creation because it has less risk of exposure and is readily available. In the patient described, Medpor would not be the most appropriate choice for the first stage of reconstruction because it is associated with a high exposure rate when used with thin atrophic or scarred soft tissue. The quality and quantity of skin redraping the auricular framework play a significant role in the aesthetics of the final result. In older patients with postablative defects and compromised surrounding tissue, prosthetic reconstruction can be offered as a viable, perhaps simplistic, solution to staged auricular reconstruction. A younger patient is seldom compliant with a prosthesis, and autologous reconstruction is a better option.
A 77-year-old man has a 12-mm squamous cell carcinoma on the lateral margin of the right helix. He is scheduled to undergo excision of the lesion with confirmation of margins by frozen section, followed by immediate reconstruction. Which of the following flaps is most appropriate for ear reconstruction?
(A) Antia-Buch flap
(B) Postauricular flap
(C) Temporoparietal fascial flap
(D) Temporalis muscle flap
The correct response is Option A.
The Antia-Buch flap is most appropriate for reconstruction of this patient’s ear defect. The lesion can be excised easily because of its location on the lateral rim and of the size of the auricle. Following excision, the resultant defect is effectively reconstructed using the Antia-Buch flap, which is a local flap that uses tissue from the helical rim based on the postauricular skin to reconstruct the helical margin. It is a reliable, single-stage procedure that is acceptable aesthetically. The surgeon may need to excise a “dog ear”-shaped area of tissue from the conchal bowl and incise and advance the helical margins separately. However, because the two ears are not viewed simultaneously, moderate differences in ear size are frequently unnoticed.
A postauricular flap does not provide thin, contoured, helical-type tissue and requires several procedures for adequate coverage. The temporoparietal fascial flap provides thin, pliable soft-tissue coverage for a cartilage or alloplastic framework, as in patients undergoing microtia reconstruction. A temporalis muscle flap is excessively bulky and is not appropriate for ear reconstruction because it would obliterate the intricate detailing of the ear.
A 6-year-old boy has prominent ears. Physical examination shows an obtuse concha-mastoid angle. The antihelical fold is normal. Which of the following is the most appropriate management?
(A) Use of a headband splint at night
(B) Use of Mustardé sutures
(C) Setback of the concha using concha-mastoid sutures
(D) Excision of excess skin
(E) Resection of the concha
The correct response is Option C.
Because prominent ears can be caused by an enlarged conchal bowl, an obtuse concha-mastoid angle, or loss of the antihelical fold, appropriate management should be based on the cause of the deformity. This 6-year-old boy has ear prominence caused by an obtuse concha-mastoid angle. Conchal setback is recommended in children to correct the enlarged conchal bowl and obtuse concha-mastoid angle deformities. This is accomplished using concha-mastoid sutures, which are mattress sutures placed between the posterior conchal wall and the mastoid periosteum to create a more acute concha-mastoid angle and decrease the height of the protruding concha.
In contrast, elliptical conchal excision may be required to perform conchal setback in adults, whose ear cartilage is typically stiff.
Ear prominence resulting from loss of the antihelical fold is best corrected by abrading or scoring the antihelix and placing Mustardé mattress sutures between the conchal eminence and the scaphoid eminence.
Splinting is effective only in infants because of the pliability of the ear cartilage in this age group.
Excess skin may need to be excised following placement of concha-mastoid sutures, but this is unlikely to produce adequate setback if performed alone. This technique is appropriate instead to decrease the prominence of the lobule or superior helix.
A 55 year old woman is referred to the office by her primary physician because she has had a painful, chronic area of scabbing on the right ear for the past three months. Physical examination shows a 2 x 1-mm area of skin ulceration on the superior helix of the ear. Surrounding inflammation and exposed cartilage are noted. Which of the following is the most appropriate initial step in management?
(A) Daily wound dressing with bacitracin ointment and avoidance of pressure on the ear
(B) Excision with 5-mm margins and coverage with a retroauricular trap door flap
(C) Excision with 5-mm margins and reconstruction with an Antia €‘Buch advancement flap
(D) Excisional biopsy and primary wound closure
(E) Injection of triamcinolone and daily topical application of hydrocortisone cream
The correct response is Option D.
The patient described most likely has a benign condition referred to as chondrodermatitis nodularis helicis, an inflammation of the cartilage of the ear that often leads to a painful open area. This condition can mimic a skin cancer on physical examination. Unless the area is clearly benign, biopsy is warranted to rule out skin cancer. Recurrence rate for this condition is high. Excisional biopsy and primary wound closure will give a pathological confirmation and may suffice as treatment.
Daily wound dressing with bacitracin ointment or injection of triamcinolone and daily topical application of hydrocortisone cream are both inappropriate because neither would give the appropriate tissue diagnosis. Excision and reconstruction or coverage with a flap are unwarranted given no pathological diagnosis.
Chondrodermatitis nodularis helicis is a condition of unknown etiology predominantly found in older men and often is associated with trauma from sleeping. It begins as an area of cartilage inflammation and then ulcerates through the skin. The treatment is excision of the cartilage and closure of the skin. Recurrence rates remain high. Preventive measures to decrease the recurrence rate include avoidance of sleeping on the affected ear.
Microtia is an auricular deformity most commonly found in patients with which of the following syndromes?
A ) Apert
B ) Binder
C ) Crouzon
D ) Pfeiffer
E ) Treacher Collins
The correct response is Option E.
Treacher Collins syndrome is characterized by bilateral abnormalities of structures within the first and second branchial arches. Treacher Collins syndrome has anomalies in structures derived from the first branchial arch, groove, and pouch. It is considered to be autosomal dominant in its inheritance with variable expressivity. Features include a convex facial profile with a retrusive lower jaw and chin, down-slant of the palpebral fissures, lower eyelid colobomas, partial absence of eyelid cilia, absent or malformed external ears, hypoplasia of the malar bones, and variable cleft palate.
Binder syndrome is characterized by nasomaxillary hypoplasia. Apert, Crouzon, and Pfeiffer syndromes are all craniosynostotic syndromes that result in mid-facial hypoplasia and a concave facial profile of varying degrees. These syndromes do not typically present with microtia.
Which of the following newborns would be the best candidate for ear molding?
A) One-day-old newborn with helical rim deformation
B) One-day-old newborn with helical rim malformation
C) One-week-old newborn with conchal deformation
D) One-week-old newborn with conchal malformation
Please note: Upon further review, this item was not scored as part of the examination.
The correct response is Option C.
The correct response is a patient with ear deformation at 1 week of age. When deciding on molding, the first question to ask is what is the difference between malformation and deformation. An ear malformation is when there is a partial absence of either the skin or cartilage of the external ear. These patients tend to be less optimal candidates for molding. Patients with ear deformations have fully developed but misshapen ears and therefore are better candidates for molding. The plasticity of the cartilage is due to maternal circulating estrogen which peaks at day 3 and returns to baseline at week 6, and up to 30% of infants will self correct in the first week of life. One-day-old is too soon to begin molding because in 24 hours, some of these deformities will spontaneously resolve.
A 25-year-old man has complete loss of the upper two-thirds of the right ear two years after sustaining a burn injury to the ear. On examination, the ear lobe and lower part of the conchal cartilage are viable and have adequate skin coverage; the ear canal is open. Scarred skin surrounds the ear remnant.
Which of the following is the most appropriate operative procedure for correction of this patient’s deformity?
(A) Creation of the upper ear with a rib cartilage framework and coverage with a local skin flap
(B) Creation of the upper ear with a rib cartilage framework and coverage with a pre-expanded local skin flap
(C) Creation of the upper ear with a rib cartilage framework and coverage with a temporoparietal fascial flap and a split-thickness skin graft
(D) Creation of the upper ear with a Silastic framework and coverage with a local skin flap
(E) Creation of the upper ear with a Silastic framework and coverage with a temporoparietal fascial flap and a split-thickness skin graft
The correct response is Option C.
The most appropriate surgical procedure for correction of this patient’s deformity is creation of the upper ear using a rib cartilage graft and coverage with a temporoparietal fascia flap and a split-thickness skin graft. These procedures will most likely result in a satisfactory outcome for this difficult reconstructive problem. The rib cartilage can be carved into an appropriate framework and covered with a thin temporoparietal fascia flap; a thin split-thickness skin graft can be used to create the intricate detail of the external ear. When successful, this reconstruction will be durable and long-lasting.
Local skin is the coverage material of choice in classic microtia reconstruction; however, when the ear remnant is surrounded by scarred skin, as in this patient with a burn injury, it will not stretch adequately to cover the framework and show detail. Skin expansion will fail because scarred skin expands poorly.
Silastic frameworks can give good early results but are not long-lasting. Because even the most minor trauma or wound problem can lead to total loss of the reconstruction, Silastic frameworks are not a good choice for reconstruction.
During second-stage ear reconstruction with elevation of the costal cartilage framework, a temporoparietal flap is elevated to cover a cartilage block. The blood supply of this flap most commonly comes from which of the following arteries?
A) Angular
B) Maxillary
C) Occipital
D) Posterior auricular
E) Superficial temporal
The correct response is Option E.
Elevation of the ear reconstruction framework can be covered by using a temporoparietal flap (TPF) if needed. The most common blood supply of the TPF is typically the superficial temporal artery but less frequently can be the posterior auricular artery or the occipital artery branches. The TPF flap can be safely raised on these less common pedicles as needed.
An 8-year-old boy is brought to the office with a congenital abnormality of the ear. A photograph is shown. When the ear is pulled on traction, the upper pole cartilage becomes visible under the skin. This abnormality is most likely caused by which of the following?
A) Anomaly of the intrinsic postauricular muscles
B) Effacement of the scaphofossa
C) Formation of a third antihelical crus
D) Hemifacial microsomia
E) Intrauterine pressure
The correct response is Option A.
This patient has cryptotia of the ear. It is also known as pocket ear. The upper part of the ear is adherent and the cartilage is buried under the skin in a pocket. Other deformities may be present, such as a missing upper sulcus, underdeveloped scapha, and antihelical crura.
It is caused by an anomaly of the intrinsic oblique and transverse auricular muscles.
Surgical treatment requires release from the pocket and resurfacing of the post- and retroauricular defects. In some cases otoplasty may be required for normalization. A number of techniques are described.
Intrauterine pressure may cause ear deformities, which may spontaneously resolve or are amenable to neonatal molding techniques. It does not cause cryptotia.
Stahl ear is associated with formation of a third antihelical crus.
Hemifacial microsomia is associated with microtia. Microtia is sometimes the only manifestation of hemifacial microsomia, but subtle clinical findings are often present, such as mild facial nerve weakness or soft tissue hypoplasia on the involved side.