Cardiology - Transportation Of The Great Arteries

Question 1

Definition

Answer 1

Aorta rises from right ventricle and pulmonary artery from left ventricle
- More common in males
- Mum >40
- Rubella
- Maternal diabetes
- Alcohol consumption

Question 2

Epidemiology

Answer 2

• More common in males
• Mum >40
• Rubella
• Maternal diabetes
• Alcohol consumption

Question 3

Pathophysiology

Answer 3

Deoxygenated blood delivered systemically
Mixing needs to be possible to sustain life: patent foramen ovale, VSD or patent ductus arteriosus must be present alongside

Question 4

Signs and symptoms

Answer 4

• Cyanosis in the first 24 hours of life
• Right ventricular heave
• Loud S2 heart sound
• Systolic murmur if VSD present
• Sometimes PD/VSD can make symptoms however within a few weeks they will develop respiratory distress, poor feeding etc

Question 5

Diagnosis

Answer 5

Low SATS
- Echo
- CXR: ‘egg on a string’ = narrowed mediastinum and cardiomegaly
- Metabolic acidosis

Question 6

Treatment

Answer 6

PGE1 infusion to ensure PDA and mixing of blood Surgical correction before 4 weeks