teratology of fallot Flashcards
1
Q
what
A
VSD
overrriding aorta
pulmonary stenosis
R ventricular hypertrophy
2
Q
risk factors
A
rubella infection
inc maternal age
alcohol consumption in pregnancy
diabetic mother
3
Q
Ix
A
ECHO
4
Q
CXR finding
A
boot shaped heart due to R ventricular thickening
5
Q
features
A
picked up antenatelly cyanosis clubbing poor feeding + weigh gain ejection systolic murmur Tet spells
6
Q
Tet spells
A
intermittent symptomatic periods where R to L shunt becomes worse, precipitating a cyanotic episode
7
Q
Tet spells - why
A
pulmonary vascular resistance increases or systemic resistance decreases
e.g. exerting themselves
8
Q
Tet spells - treatment options
A
older kid can squat
younger kid sit with knees to chest
oxygen beta blockers IV fluids to inc preload morphine sodium bicarbonate - buffer acidosis phenylephrine infusion - inc systemic resistance
9
Q
management
A
prostaglandin infusion to maintain ductus arteriosus
total surgical repair
