Esophagus Path I Flashcards
VACTERL association
vertebral anomalies anal atresia cardiac defects TEF/esophageal atresia renal and radial abnormalities limb defects
non random birth defects - cause of association unknown
salivation, choking, vomiting, cyanosis with feeding
TEF - tracheoesophageal fistula
polyhydramnios in utero
esophageal atresia
most common congenital esophagus defect
blinding ending superior esophagus
fistula of trachea to lower esophagus
most common intestinal atresia
imperforate anus
pyloric stenosis
projectile vomiting 2 to 8 weeks of age
males
hypertrophied smooth m spasm on emptying of stomach
hypokalemic hypochloremic metabolic alkalosis
with pyloric stenosis - loss of gastric acid
also secondary hyperaldosteronism with hypovolemia
nipple sign
seen with pyloric stenosis
tx of pyloric stenosis
cut smooth m. to correct stenosis
double bubble
duodenal atresia
and annular pancreas
duodenal atresia
trisomy 21
majority below ampulla of vater
double bubble
low lesion imperforate anus
colon close to skin
common in females
anal stenosis or rectum ends in blind pouch
high lesion imperforate anus
colon higher up in pelvis
-fistula to bladder, urethra, vagina
look for other congenital defects
like VACTERL association
anoplasty
tx of imperforate anus
-making a new butthole
persitant cloaca
rectum, vagina, urinary tract joined in single tract/channel
diaphragmatic hernia
incomplete formation of diaphragm
-with pulmonary hypoplasia
bochdalek hernia
postero-lateral hernia
- more common
- majority on left side
morgagni hernia
anterior defect of hernia
-adjacent to xiphoid of sternum
diaphragm eventration
abnormal displacement of diaphragm
-results in pulmonary hypoplasia and HTN