Cystic fibrosis Flashcards
1
Q
Cystic fibrosis
A
- Genetic disorder that effects the lungs, pancreas, liver and reproductive organs
2
Q
Clinical signs of pulmonary disease
A
- Reoccourant infections and production of opious viscous sputum and malabsorbtion due to pancreatic deficiency
3
Q
Aims for the treatment of cystic fibrosis
A
- Prevent and manage lung infections
- Loosen and remove thick stick mucus from the lungs
- Preventing and treating intestinal obstructions
- Provide sufficent nutrition and hydration
- Optimise lung function
4
Q
Non-drug treatments for cystic fibrosis
A
- Airway clearing, nebuliser use and physical activity
- Regular exercise to improve lung function and fitness
5
Q
Drug treatment for cystic fibrosis
A
- Prevention of lung infection and maintainance of lung function
- Lung disease must have routine review based on clinicl condition
- Adults every 3 month review
- More frequent review after diagnosis
6
Q
Mucolytics
A
- Lung disease + cystic fibrosis offered this
- Dornas alfa is the first choice then add hypertonic sodium chloride if inadequate or just hypertonic sodium chloride
- Mannitol powder inhalation when dornas alfa doesnt work and lung function rapidly declines
7
Q
Staphylococcus aureus
A
Offer an antibacterial oral or IV
8
Q
Pseudomonas aeruginosa
A
Offer an oral antibacterial in
combination with an inhaled antibacterial
9
Q
Aspergillus fumigatus complex
A
- Offer an antifungal drug only to
suppress chronic complex respiratory infection in patients with declining pulmonary status
