Cyanotic heart defect Flashcards
What are the cyanotic heart defects
tertraology of fallot
transposition of great vessels
persistent truncus arteriosus
tricuspid atresia
total anomalous pulmonary venous return
What is the physiology of the cyanotic defects:
right to left shunting
Explain the tetraology of fallot (4)
- pulmonic stenosis
- overriding aorta
- VSD
- RV hypertrophy
symptoms of tetraology of fallot
tet spells
harsh systolic ejection murmur, LUSB
left upper sternal border! (upper, think pulmonic)
xray findings for tetraology of fallot
boot shaped heart
associations of tetraology of fallot (risk factors)
digeorge, down syndrome, fetal alcohol syndrome
compensation for tet spells
knee to chest (squatting)
pathophysiology of transposition of great vessels
failed spiraling of aorticopulmonary septum: reversal of pulmonary artery and aorta: two parallel circuits: RV-> aorta and LV- PA
Chest xray on T of Great Vessels findings
egg on a string.
management of T o Great Vessels
PGE1->surgery
Transposition of great vessels is associated with condition
maternal diabetes
persistent trucus arteriosus- pathophysiology
partial incomplete aorticopulmonary septum formation, failure of neural crest cell migration: mixing of all oxygenated and deoxygenated blood at the ventricles and VSD.
Which heart conditions are associated with DiGeorge
Tetraology of Fallot
Persistent Trucus Arteriosus
What is tricuspid atresia
absent tricuspid valve
explain the pathophysiology of tricuspid atresia
because theres no tricuspid valve, it becomes a massive atria (RV hypoplasia) and this is known as right atrialization
RV atrialization is what
RV hypoplasia: associated with tricuspid atresia
ebstein anomaly- lithium exposure is associated with what?
tricuspid atresia
Ebstein anomaly is associate with arrhythmia
wolf parkinson white
what it total anamalous pulmonary venous return?
pulmonary veins draining into the wrong spot- putting it into the right atrium. they will benefit a shunt (ASD)
What is the xray finding for TAPVR?
snowman sign
what is the presentation of total anomalous pulmonary venous return
increase in pulmonary pressures
–>pulmonary hypertension
