West Syndrome (infantile Spasms) Flashcards
What is west syndrome?
A type of childhood epilepsy
What is another name for West syndrome?
Infantile spasm
When does West syndrome typically occur?
In the first 4-8 months of life
Who are more commonly affected by West syndrome?
Male infants
What is West syndrome associated with?
A serious underlying condition
Developmental regression and high morbidity.
Does West syndrome have a good prognosis?
No
What is the characteristic feature of West syndrome?
Characteristic ‘salaam’ attacks:
What is a Salaam attack?
Flexion of the head, trunk and arms followed by extension of the arms
How can the seizures also be described in someone with West syndrome?
Myoclonic jerking, referred to as ‘jack knife’ spasms that occur in clusters
How long do the seizures last in someone with West syndrome?
Only 1-2 seconds but may be repeated up to 50 times
What progressively occurs in someone with West syndrome?
Progressive mental handicap
How is West syndrome diagnosed?
History
Characteristic EEG
CT
What can be seen on an EEG of someone with West syndrome?
Hypsarrhythmia
What might a CT show in someone with West syndrome?
Diffuse or localised brain disease
What brain disease can be shown on a CT of someone with West syndrome?
Tuberous sclerosis
