Ebstein’s Anomaly Flashcards
What type of condition is Ebstein’s Anomaly?
Congenital heart defect
What is Ebstein’s anomaly characterised by?
Low insertion of the tricuspid valve
What does low insertion of the tricuspid valve result in?
Bigger right atrium and a smaller right ventricle.
What does a bigger atrium and a smaller ventricle result in?
Poor flow from the right atrium to the right ventricle
Therefore poor flow to the pulmonary vessels.
What can poor flow to the pulmonary vessels result in?
cyanosis
What is Ebstein’s anomaly also associated with?
Wolff-Parkinson-White syndrome.
What is a possible cause of Ebstein’s anomaly?
Exposure to lithium in utero
What are the possible cardiac presentations of Ebstein’s anomaly?
- prominent ‘a’ wave in the distended jugular venous pulse,
- tricuspid regurgitation
- pansystolic murmur, worse on inspiration
- right bundle branch block → widely split S1 and S2
What would you hear on auscultation of someone with Ebstein’s anomaly
Gallop rhythm heard on auscultation characterised by the addition of the third and fourth heart sounds
How can Ebstein’s anomaly present?
- Cyanosis
- Shortness of breath and tachypnoea
- Poor feeding
- Collapse or cardiac arrest
What is seen in at least 80% patients with Ebstein’s anomaly?
Patent foramen ovale (PFO)
or
Atrial septal defect (ASD)
What is the investigation of choice for Ebstein’s anomaly?
Echocardiogram
What is the definitive management of Ebstein’s anomaly?
Surgical correction of the underlying defect.
What is the medical management of Ebstein’s anomaly?
Treating arrhythmias and heart failure.
Why might you give prophylactic antibiotics?
To prevent infective endocarditis.
