Test 4 part 3 Flashcards
CCHD physiological consequences
Cyanosis
Hypoperfusion
Respiratory distress and failure to thrive
Underdevelopment of the left side of the heart which can include the left ventricle, aortic valve and ascending aorta.
Most severe left sided obstruction lesion
All of RV is pumped to PA
Descending aorta and coronary arteries supplied by PDA
Hypoplastic left heart syndrome
Hypoplastic left heart syndrome treatment
Prostaglandins
Norwood operation
Cardiac transplantation
Small or absent pulmonary valve with no ability to shunt through VSD or ASD (septum is intact)
Affects ability to pump blood to lungs
Pulmonary artresia with intact septum
A hole in the wall between the two lower ventricles of the heart
A narrowing of the pulmonary valve and main pulmonary artery
The aortic valves which opens to the aortas is enlarged and seems to open from both ventricles
The muscular wall of the lower right chamber of the heart (right ventricle) is thicker than normal
Tetralogy of Fallot (TOF)
Blood returning from the body bypasses the lungs and is pumped back out to the body
This occurs because the main connections are reversed
Most common cyanotic CCHD
Associated with maternal diabetes
TGA (Transposition of the Great Arteries)
A defect with multiple variations in which the veins carrying O2 rich blood do not connect with the left side of the heart
PV return to right side of heart
Snowman sign
Total anomalous pulmonary venous return (TAPVR)
Treatment for TAPVR
Emergency surgery in patient with venous obstruction
Require eventual heart-lung transplant
One large artery arises from the heart instead of a separate pulmonary artery and aorta
Always accompanied by VSD
Single loud heart sound
Diastolic murmur at LSB
Truncus arteriosus
Male predominance and assoc. w/ Turner’s syndrome (XO) and PHACE syndrome (multiple defects- posterior fossa brain, large hemangioma, arterial lesions, coarctation, eye defects)
Obstruction occurring almost exclusively at the ductus arteriousus
Lower BP in lower body
Coarctation of aorta
Treatment for coarctation aorta
PGE for short term PDA
Surgery
Closure of PDA leads to
cariogenic shock
atresia is
no opening
Tricuspid valve is not open which leads to no flow of blood from R atrium to R ventricle
Tricuspid atresia
When the valve that controls blood flow from the heart to the lungs doesn’t form at all. This valve controls blood flow from the right ventricle to the main pulmonary artery (the blood vessel that carries blood from the heart to the lungs). This can occur with a VSD.
Pulmonary atresia
what is used to keep PDA open
prostaglandin E
Treatment for pink baby defects, PDA, ASD, VSD (without other defects)
NSAIDS and CCB
allow blood to pass from the left to the right side of the heart. The oxygen-rich blood then gets pumped back to the lungs instead of out to the body, causing the heart to work harder
ASD and VSD
congenital heart defect diagnostic tests
Arterial blood gas analysis
Umbilical arterial catheter
Chest x ray
Echocardiogram
Multiples pregnancies babies are at risk for
Mental retardation
Cerebral palsy
Vision/ hearing loss
How often do women need to visit if they are pregnant with multiples at 12-14 weeks
twice per month
when do weekly visits start for mothers pregnant with multiples
24 weeks
when do biweekly non-stress tests start for a mother pregnant with multiples
32 weeks
what week do mothers pregnant with multiples need to increase risk
30 weeks