Pediatrics: Gastrointestinal, Luminal Flashcards
Frontal chest radiograph with an NG tube stopped in the upper neck…
Think tracheoesophageal fistula/esophageal atresia
What is the most common subtype of esophageal atresia/tracheoesophageal fistula?
N-type fistula (85%)
Note: This is a blind ending upper esophagus with the lower esophagus communicating with the trachea.
H-type esophageal atresia
When the entire esophagus is present, but there is also a tracheoesophageal fistula
How do you diagnose esophageal atresia/tracheoesophageal fistula?
Fluoroscopic swallow study
Esophageal atresia/tracheoesophageal fistula is associated with…
VACTERL:
- Vertebral anomalies
- Anus, imperforate
- Cardiac anomalies
- Tracheoesophageal fistula/Esophageal atresia
- Renal anomalies
- Limb anomalies
Excessive air in the stomach in a newborn…
Think tracheoesophageal fistula (classically H-type, but also seen with N-type)
What are the major subtypes of tracheoesophageal fistula?
- N-type (blind ending upper esophagus; lower esophagus connects to the trachea)
- Esophageal atresia (blind-ending upper esophagus without any connection to the trachea)
- H-type (full esophagus with additional tracheoesophageal fistula)
No air in the stomach of a newborn…
Think esophageal atresia
What imaging finding should be mentioned (if present) prior to repair of a tracheoesophageal fistula?
Right aortic arch (changes surgical approach)
VACTERL
A collection of congenital anomalies that are highly associated:
- Vertebral anomalies (37%)
- Anus, imperforate (63%)
- Cardiac anomalies (77%)
- Tracheoesophageal fistula/Esophageal atresia (40%)
- Renal anomalies (72%)
- Limb anomalies (58%)
Diagnosis of VACTERL
When 3 or more of the VACTERL anomalies are found in a pt
Which of the VACTERL anomalies are the most common to find?
- Cardiac (77%)
- Renal (72%)
Major complication of esophageal atresia repair
Focal anastomotic stricture (occurs in 30% of cases)
A coin is present at the level of the thoracic inlet and appears linear (not round) on a frontal chest radiograph. Where is it?
Trachea, the flexible posterior membrane causes coins to orient in the sagittal plane
Note: If it appears round on frontal radiograph, it is more likely in the esophagus.
Why are pennies minted after 1982 a more problematic foreign body than other coins?
Pennies minted after 1982 are mostly made of zinc, which can cause gastric ulcerations when exposed to stomach acid
Note: Pennies minted before 1982 were made of copper, which is relatively safe.
Management of ingested AA or AAA batteries
Serial plain films and extraction if they stay in the stomach for more than 2 days
Management of ingested disc battery
Emergency removal if in esophagus (within 2 hours)
Urgent/emergent removal from stomach (within 12 hours)
Name the vascular impression
Pulmonary sling (the only variant that goes between the esophagus and the trachea)
Name the vascular impression
Double aortic arch
Name the vascular impression
Innominate artery compression
Name the vascular impression
Left arch with aberrant right subclavian
OR
Right arch with aberrant left subclavian
Pulmonary sling has a high risk of…
Tracheal stenosis
Note: The pulmonary sling is when the left pulmonary artery arises from the right pulmonary artery and then runs between the trachea and esophagus.
Treatment of pulmonary sling
Surgical repositioning of the malpositioned left pulmonary artery (to avoid tracheal stenosis)
What is the most common symptomatic vascular ring?
Double aortic arch
Diverticulum of Kommerell
A pouch like aneurysmal dilatation of the origin of an aberrant right subclavian artery
Dysphagia lusoria
Dysphagia secondary to an aberrant right subclavian artery
Differential for high bowel obstruction in the neonate
- Midgut volvulus/malrotation
- Duodenal atresia
- Duodenal web
- Annular pancreas
- Jejunal atresia
Differential for low bowel obstruction in the neonate
- Hirschprung disease
- Meconium plug syndrome
- Ileal atresia
- Meconium ileus
- Anal atresia/colonic atresia
Neonatal radiograph demonstrates absent bowel gas except for a single bubble in the left upper quadrant…
Think gastric (astral or pyloric) atresia
Neonatal radiograph demonstrates absent bowel gas except for a double bubble in the left upper quadrant…
Duodenal atresia
Note: The “double bubble” sign without any distal gas is highly specific for duodenal atresia. Any distal gas excludes duodenal atresia.
Jejunal atresias are associated with…
Other atresias (e.g. colonic atresia)
Note: Jejunal atresia is usually due to a vascular insult during development that causes multiple atresias.
Neonatal radiograph demonstrates prominent gastric bubble with some distal air in a newborn with bilious vomiting…
Suspicious for midgut volvulus, recommend emergent upper GI study
Neonatal radiograph demonstrates a “double bubble” in the left upper quadrant with scant gas distally…
Think duodenal web, duodenal stenosis, or midgut volvulus and recommend an upper GI series
Note: Any distal gas, even small volumes, excludes duodenal atresia.
Neonatal radiograph demonstrates diffusely dilated loops of bowel…
Think low obstruction (e.g. ileum or large bowel) and recommend a contrast enema (if normal, then get upper GI to exclude atypical midgut volvulus)
Third trimester ultrasound demonstrates “double bubble” appearance in fetal left upper quadrant…
Duodenal atresia
Neonatal upper GI
Corkscrew duodenum, diagnostic of midgut volvulus (surgical emergency)
What should you look for on a neonatal upper GI series?
- Does contrast opacify the entire duodenum (if not, think duodenal obstruction)
- Does the duodenum pass the midline to the left hemiabdomen (if not, think malrotation/volvulus)
- Is there a corkscrew appearance of the duodenum (midgut volvulus)
Malrotation is associated with a high risk of what complications?
Midgut volvulus and internal hernias
Note: They can also get intermittent duodenal obstruction due to compression from Ladd’s bands.
Malrotation is associated with…
- Heterodoxy syndrome
- Omphaloceles
On US or CT, the SMA is to the right of the SMV…
Malrotation
1 month old with non bilious vomiting…
Think hypertrophic pyloric stenosis and recommend an ultrasound
Infant with bilious vomiting…
Think midgut volvulus and recommend emergent upper GI series
Ladd’s bands
Fibrous bands attaching the cecum to the abdominal wall that can cause intermittent obstruction in the setting of malrotation
Ladd’s procedure
Treatment for malrotation (surgical disruption of the Ladd’s bands that predispose to duodenal obstruction and midgut volvulus)
Preduodenal portal vein
An anatomic variant where the portal vein sits anterior to the 2nd part of the duodenum
Note: This is associated with duodenal obstruction 50% of the time secondary to Ladd’s bands, annular pancreas, or other causes of duodenal obstruction.
Causes of partial duodenal obstruction in a neonate
Extrinsic compression (Ladd’s bands in malrotation, annular pancreas)
Intrinsic narrowing (duodenal web, duodenal stenosis)
When does hypertrophic pyloric stenosis occur?
2-12 weeks of age (peak 3-6 weeks)
Note: NOT before 2 weeks and not after 3 months.
Ultrasound criteria for hypertrophic pyloric stenosis
4 mm single wall thickness and length of at least 14 mm
What is the main differential diagnosis for hypertrophic pyloric stenosis on ultrasound?
Pylorospasm (which should relax during the exam; true hypertrophy will not relax)
What is a major cause of false negatives on US for hypertrophic pyloric stenosis?
Gastric over distention (which can displace the gastric antrum/pylorus)
Organoaxial gastric volvulus
The greater curvature flips over the lesser curvature (rotation around the long axis)
Note: This type is mainly seen in older pts with paraesophageal hernias.
Mesenteroaxial gastric volvulus
Twisting of the mesentery so that the gastric antrum flips up over the GE junction (rotation around the short axis)
Note: This type is more common in kids and requires surgical correction.