HYPERTROPHIC CARDIOMYOPATHY Flashcards
1
Q
name this disease?
genetically determined heart muscle disease that affects the contractile apparatus
different phenotypes and clinical manifestations
most HCM disease occurs in childhood and adolescence
A
hypertrophic cardiomyopathy
2
Q
pathophysiology of HCM?
A
myocyte hypertrophy with expanded EC matrix
LV wall thickness
3
Q
symptoms?
A
fatigue
dyspnea
chest pain
palpitations
increased risk of: sudden cardiac disease
*some patients have no minor symptoms
4
Q
HCM can progress to?
A
HCM with LV systolic dysfunction
HCM with diastolic dysfunction
ventricular arrhythmias
prophylactic ICD placement for primary prevention of SCD
5
Q
management?
A
implantation of ICD is best therapy
avoid sports
symptom control with beta blockade or amiodarone
heart transplant is an option
- refractory heart failure
- intractable dysrhythmias
