ESCLEROSIS SISTEMICA PROGRESIVA Flashcards

1
Q

DEFINICION

A

Enfermedad autoinmune sistemica crónica caracterizada por cambios atroficos y fibroticos de la piel, arterias digitales, membrana sinovial y órganos

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

SUGRUPOS

A

Esclerosis sistemica con afectacion cutanea difusa
Esclerosis sistemica con afectacion cutanea limitada

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

Esclerosis sistemica con afectacion cutanea difusa

A

Induración cutanea extensa que comienza en dedos

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

Esclerosis sistemica con afectacion cutanea LIMITADA

A

Sindrome CREST: Calcinosis, Reynauld, Afectación esofágica, Esclerodactilia, telangiectasias

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

EPIDEMIOLOGIA

A

Mujeres 40 años
Raza negra

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

ETIOPATOGENIA

A

HLA-DR1, 3 y 5
Factores ambientales

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

Manifestaciones cutaneas

A

Endurecimiento de la piel de zonas proximales de articulaciones metacarpofalangicas (acrosclerosis)
1. Fase edematosa
2. Fase indurativa
3. Fase atrofica

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

MANIFESTACIONES REUMATOLOGICAS

A

Artralgias en grandes y pequeñas articulaciones
Rigidez articular
Crepitacion correosa
Afectacion tendinosa
Sindrome de tunel carpiano

How well did you know this?
1
Not at all
2
3
4
5
Perfectly