Dermatology

Question 1

What are the features of ectodermal dysplasias?

Answer 1

Absent, sparse or slow growing hair
Widely spaced, conical teeth
Dysplastic nails
hypohydratic +/- scaling skin

Question 2

Describe epidermolysis bullosa simplex

Answer 2

A.D.
Either neonate with blisteriong on pressure areas or older child with blistering to hands and feet on crawling

Question 3

Describe Junctional epidermolysis bullosa

Answer 3

A.R.
Skin errosions and excessive granulations around face.
Nails dystrophic or absent

Question 4

Describe Dystrophic epidermolysis bullosa

Answer 4

Severe and large area of skin lost at birth
Extensive erosions can lead to scarring, contracture and mitten deformity

Question 5

Describe Inconteinentia pigmenti

Answer 5

X-linked dominant
MAles die in utero
Swirling hyperpigmented skin lesions from birth

Question 6

Describe course of haemangiomas

Answer 6

Rapid growth 4-6 weeks, max size 3 months.
Natural involution and regression from 12 months.

Question 7

What haemangiomas require treatment and describe that treatment

Answer 7

> 20 cm or with plaque. Propranolol.
Needs ECG, HR and BP monitoring beforehand

Question 8

Describe candida nappy rash

Answer 8

Multiple erythematous circular satellite type lesions affecting groin and buttocks

Question 9

What skin condition is associated with coeliac disease?

Answer 9

Dermatitis herpetiformis
Erythematous, itchy, blistering

Question 10

describe erythema nodosum

Answer 10

Erythematous, hot, painful nodules classically on shins and ankles

Question 11

What is the dermatological manifestation of langerhans cell histiocytosis?

Answer 11

Greasy papules on scalp, neck, axillae and groin

Question 12

What is the dermatological manifestation of scleroderma?

Answer 12

Morphoea. Thickening and hardening of skin due to collogen deposition.

Question 13

What are condylomata acuminata?

Answer 13

Anogenital warts - think sexual abuse