CF - Mx

Question 1

Ix

• bloods - fbc, ?, ?, ?
• ? ? test - levels >?mmol/L are characteristic
• annual ? screening
• sputum ?
• CXR - ?, evidence of ?
• abdo ? - ? liver/cirrhosis, chronic ?
• ? - obstructive defects

Answer 1

u+e, lft, clotting
na sweat, 70 (also referred to as chloride sw test)
diabetic
culture
hyperinflation
bronchiectasis
USS
fatty
pancreatitis
spirometry

Question 2

Mx
-? based, specific attention to ? and ? health

must not forget to treat their ? if they have it, to treat their ? if have it, and to offer genetic ?

Answer 2

MDT
psychosocial
physical

DM
infertility
counselling

Question 3

Chest mx 1

• as per bronchiectasis - with ?, ? and bronchodilators
• two parenteral ? are used for exacerbations (to decr ?, often one with ? cover) - experts may decide to employ regular prophylaxis with ?

Answer 3

ABx, physio
Abx, resistance,
PA
azithromycin

Question 4

Chest mx 2

• ? - DNase ? nebs
• ? ? devices - eg acapella - look for at bedside
• ? ? if resp failure develops

Answer 4

mucolytics, daily
airway clearance
lung transplant

Question 5

Gi mx

• ? ? replacement (creon)
• fat ? ? supplementation (????)
• liver transplant for advanced ?

Answer 5

panc enzyme
sol vits , ADEK
cirrhosis