Mucinoses

Question 1

Primary dermal mucins under normal conditions

Answer 1

Sulfated mucopolysaccharides - chondroitin sulfate and heparin sulfate

Question 2

Increased mucin in the skin (besides obvious like SLE)

Answer 2

Degos, PUVA, retinoids

Question 3

MC organ involved in scleromyxedema

Answer 3

GI

Question 4

May be associated with scleromyxedema

Answer 4

Hep C, raynauds, dysphasia, carpal tunnel (making it hard to distinguish from scleroderma)

Question 5

Follicular mucinosis

Answer 5

Mucin accumulates in sebaceous gland and ORS.

Syringolymphoid hyperplasia should raise concern for lymphoma

*sensory disturbance may be noted

Tx- spontaneous involution may occur in kids, topical steroids, plaquinel

Question 6

Follicular MF

Answer 6

Worse prognosis than classic CTCL

Question 7

Myxoid cysts

Answer 7

May occur subungual, proximal nail file, DIP
No true lining
F > M and OA is frequently seen in the DIP
If able to reduce then they connect to joint space

Question 8

Multiple myxoid cysts seen in

Answer 8

CTD