MOTOR NEURONE DISEASE

Question 1

X

Answer 1

C

Question 2

C

Answer 2

C

Question 3

C

Answer 3

C

Question 4

C

Answer 4

C

Question 5

Motor neuron disease rarely presents before

Answer 5

40 years

Question 6

G

Question 7

Symptoms of motor neurone disease?

Answer 7

Sensation intact ! cranial nerve normal

some limbs demonstrating hypotonia and some hypertonia.- asymmetric limb weakness

fasciculations!!!!!!

reflexes is variable, with some limbs demonstrating hyperreflexia and hyporeflexia in different nerve roots in the same limb.

upgoing plantars

Question 8

other features we must now in MND ?

Answer 8

doesn’t affect external ocular muscles
no cerebellar signs
abdominal reflexes are usually preserved and sphincter dysfunction if present is a late feature

Question 9

V

Question 10

C

Question 11

what is Amyotrophic lateral sclerosis

Answer 11

rare neurological disease that affects motor neurons

Question 12

C

Question 13

V

Question 14

V

Question 15

V

Question 16

V

Question 17

B

Question 18

H

Question 19

H

Question 20

Management of motor neurone disease ?

Answer 20

Riluzole
prevents stimulation of glutamate receptors
used mainly in amyotrophic lateral sclerosis
prolongs life by about 3 months

Respiratory care
non-invasive ventilation (usually BIPAP) is used at night
studies have shown a survival benefit of around 7 months= most effective

Nutrition
percutaneous gastrostomy tube (PEG) is the preferred way to support nutrition and has been associated with prolonged survival