Cystic Fibrosis Flashcards
What is the energy requirement for individuals with cystic fibrosis compared to typical needs?
110–200% higher energy requirements due to increased metabolic demands.
Why is PERT used in cystic fibrosis?
Sticky mucus blocks the passage of enzymes from the pancreas to the small intestine, impairing digestion.
What is the typical PERT dosage for meals and snacks?
Meals: 50,000 units; Snacks: 25,000 units.
True or False: Fat intake should be restricted for individuals with cystic fibrosis.
False. Fat intake is generally unrestricted unless weight gain is excessive.
What diagnostic test is commonly used to identify cystic fibrosis in newborns?
Heel prick test
What are some common nutritional deficiencies or risks associated with CF?
Vitamin A deficiency
Osteoporosis
Risk of fat-soluble vitamin deficiencies (A, D, E, K)
What disorders are associated with CF?
Individuals with cystic fibrosis often have GI comorbidities, diabetes, and bone disorders.
What specific supplements may be required for cystic fibrosis patients?
Fat-soluble vitamins (A, D, E, K)
Iron (Fe)
Calcium (Ca)
Increased dietary energy requirements for cystic fibrosis patients range from _____% to _____% of typical needs.
120% to 150%.
Why is increased salt intake often recommended for CF?
To compensate for high salt losses due to excessive sweating.
What is the role of PERT in managing pancreatic insufficiency in cystic fibrosis?
PERT provides the enzymes needed for proper digestion and nutrient absorption when the pancreas cannot produce them adequately.
