Congenital Heart Disorders Flashcards
which disorders are cyanotic?
- Tetraology of Fallot
- Hypoplastic LH syndrome
- Transposition of the Great Vessels
- Pulmomary Atresia
which disorders are acyanotic?
- atrial septal defect
- ventricular septal defect
- patent ductus arteriosus
- coarctation of the aorta
Transposition of the Great Vessels
what is it?
R side (deoxy blood) pumps out to body while L side (oxy blood) pumps back into lungs
Transposition of the Great Vessels
presentation
- cyanosis/breathing probs
- poor feeding
Transposition of the Great Vessels
PE findings
- weak pulse
- ashen/blue skin
- systolic murmur
Transposition of the Great Vessels
tx
- abort
- arterial switch operation
Hypoplastic Left Heart Syndrome
what is it?
L side of heart fails to develop
Hypoplastic Left Heart Syndrome
sx
- shock
- cyanosis
- variable murmur
Hypoplastic Left Heart Syndrome
tx
3 stages of surgery
* Norwood (first 2wks of life)
* bi-directional glenn shunt (4-6 mo)
* Fontan (18 mo to 3 yrs)
Hypoplastic Left Heart Syndrome
tx if not eligible for 3 surgical steps?
transplant
Pulmonary Atresia
describe
pulm valve did not form, no flow from RV to pulm artery
Pulmonary Atresia
presentation
- cyanotic, blue
- variable murmur
- hyperdynamic apical impulse
Pulmonary Atresia
tx
- rx to keep PDA open
- usually stent PV or patch VSD
Tetralogy of Fallot
describe
- VSD
- pulm stenosis
- RVH
- overriding aorta
Tetralogy of Fallot
presentation
- cyanosis
- polycythemia
- agitation
Tetralogy of Fallot
describe the murmur
crescendo-decrescendo holosystolic LSB radiate to back
Tetralogy of Fallot
PE findings
5
- clubbing
- tet spell (randomly passes out)
- squatting
- boot shaped heart
- nail clubbing