CJD Flashcards
1
Q
what
A
rapidly progressing neurological condition caused by prion proteins
2
Q
what do proin protiens do
A
induce formation of amyloid folds resulting in tightly packed beta-pleated sheets resistant to proteases
3
Q
features
A
rapid onset dementia
myoclonus
4
Q
Ix
A
EEG
MRI
tonsil biopsy
5
Q
EEG findings
A
biphasic high amplitude sharp waves
6
Q
MRI findings
A
hyperintense signals in basal ganglia and thalmus